Isolated pulmonary vein stenosis in complex congenital heart disease, simulating cor triatriatum by cardiac catheterization and transoesophageal echocardiography

A. H. Cromme-Diijkhuis, A. J. Bogers, J. Hess

Sophia Children’s Hospital and University Hospital.
Netherlands

European Heart Journal
Eur Heart J 1995; 16: 287-288
DOI: 10.1093/oxfordjournals.eurheartj.a060900

Abstract
A case of localized stenosis of the lower left pulmonary vein, associated with perimembranous ventricular septal defect (VSD) and secundum atrial defect (ASD), a borderline sized mitral valve apparatus and left ventricle, is described. This final diagnosis was made at surgery, as the localized stenosis of the left pulmonary vein was misinterpreted as partial cor triatriatum by cardiac catheterization, cineangiocardiography and extensive echocardiographic studies. Surgical correction of all the defects was successful, but pulmonary vascular resistance was still increased 2 years after surgery.

Category
Stenosis or Obstruction of Normal Pulmonary Venous Connections
Pulmonary Hypertension Associated with Stenosis or Atresia of Pulmonary Veins
Patient Factors Influencing the Onset, Severity or Outcome of Disease
Diagnostic Testing. Noninvasive
Diagnostic Testing. Invasive
Surgical Interventions for Pulmonary Venous Obstruction After the Onset of Disease

Year of Publication: 1995

Age Focus: Pediatric

Article Type: Case Reports or Retrospective Observations in Small Groups of Patients (≤10 patients)

Article Access: Free PDF File or Full Text Article Available Through PubMed or DOI: No