Pulmonary vein atresia with severe contralateral pulmonary vein stenosis in a child

Jeffrey E. Vergales, Shawn C. West, Andrew W. Hoyer

University of Virginia Health System
United States

Pediatric Cardiology
Pediatr Cardiol 2012; 33: 663-665
DOI: 10.1007/s00246-012-0178-y

Abstract
Unilateral pulmonary vein atresia is a very rare congenital anomaly associated with high morbidity and mortality. Most cases present in infancy or childhood with recurrent respiratory infections or hemoptysis. Further, the diagnosis can often be difficult to make. We present an infant who died due to unilateral right-sided pulmonary vein atresia in conjunction with severe contralateral pulmonary vein stenosis who was diagnosed with the assistance of cardiac computed tomography scanning.

Category
Stenosis or Obstruction of Normal Pulmonary Venous Connections
Absence or Atresia of Normal Pulmonary Venous Connections
Diagnostic Testing. Noninvasive

Year of Publication: 2012

Age Focus: Pediatric

Article Type: Case Reports or Retrospective Observations in Small Groups of Patients (≤10 patients)

Article Access: Free PDF File or Full Text Article Available Through PubMed or DOI: No