Hee Ju Hong, Hye Won Kwon, Jae Gun Kwak, Sang Yun Lee, Yoon Seong Lee
Seoul National University Hospital.
South Korea
Cardiology in the Young
Cardiol Young 2023;
DOI: 10.1017/S1047951123003724
Abstract
A 65-day-old girl presented to the emergency room with lethargy, requiring emergency venoarterial extracorporeal membrane oxygenation for refractory cardiogenic shock. Initially, hypoplastic left heart syndrome was suspected. However, cor triatriatum with a pinpoint opening on the membrane was diagnosed based on a detailed echocardiographic examination. After membrane resection, the left heart size was restored. However, follow-up echocardiography performed 4 months later showed occlusion of both upper pulmonary veins and stenosis in both lower pulmonary veins. Hybrid balloon angioplasty was performed in all pulmonary veins, and stents were inserted into the right upper and lower pulmonary veins. Despite repeated balloon angioplasty, all pulmonary vein stenosis progressed over 6 months and the patient expired while waiting for a heart-lung transplant. Even after successful repair of cor triatriatum, short-term close follow-up is required for detecting the development of pulmonary vein stenosis.
Category
Stenosis or Obstruction of Pulmonary Veins Following Surgical Repair of Cor Triatriatum
Catheter-mediated Interventions: Efficacy or Lack of Efficacy
Year of Publication: 2023
Age Focus: Pediatric
Article Type: Case Reports or Retrospective Observations in Small Groups of Patients (≤10 patients)
Article Access: Free PDF File or Full Text Article Available Through PubMed or DOI: No