Kevin Turley, William Y. Tucker, Daniel J. Ullyot. Paul A. Ebert
University of California, San Francisco
United States
American Journal of Cardiology
Am J Cardiol 1980; 45: 92-97
DOI: 10.1016/0002-9149(80)90225-8
Abstract
The factor of age has been proposed as the major determinant of survival after correction of total anomalous pulmonary venous connection; consequently, operation may be postponed and the infant’s clinical condition deteriorate. This study describes 22 infants who underwent surgical correction of this disorder in the 1st year of life between 1975 and 1978. Twelve were in the 1st month and six in the first 4 days of life. Nine had a type I, six a type II, six a type III and one a type IV lesion. The infants’ weights ranged from 2.6 to 6.9 kg (mean 4.0) at the time of operation; this fact emphasizes the retarded growth of these infants.
Nineteen of 22 infants (including all 6 infants operated on during the first 4 days of life) survived operation, yielding an 87 percent hospital survival rate. Two late deaths occurred secondary to intimal fibroplasia of the pulmonary veins proximal to the site of atrial anastomosis; this represents a potential problem especially in infants with type III lesions. The strongest determinants of survival were type of lesion, pulmonary venous obstruction and depressed left ventricular function. Age in itself is not a determinant of survival after correction of total anomalous pulmonary venous connection. The timing of corrective surgery should be influenced by the clinical condition of the infant.
Category
Stenosis or Obstruction of Pulmonary Veins Following Surgical Repair of Anomalous Pulmonary Venous Connections
Incidence or Prevalence of Disease
Length of Life Associated with Pulmonary Venous Obstruction
Year of Publication: 1980
Age Focus: Pediatric
Article Type: Retrospective Observational Cohort Studies (>10 patients)
Article Access: Free PDF File or Full Text Article Available Through PubMed or DOI: No