Pulmonary Vein Stenosis Severity Score to Predict the Outcome of Surgical Intervention (proposed by Kalfa and associates)

Each pulmonary vein is graded from 0 to 4.0

0                   No stenosis

1.0                 Mild stenosis: focal

1.5                 Mild stenosis: diffuse

2.0                Moderate stenosis: focal

2.5                Moderate stenosis: diffuse

3.0                Severe stenosis: focal

3.5                Severe stenosis: diffuse

4.0                Atresia or occlusion

The pulmonary vein stenosis severity score is the sum of scores for each vein. An additional 2 points are added if there is bilateral disease (possible range, 0–18).