Congenital stenosis of individual pulmonary veins: clinical spectrum and unsuccessful treatment by transvenous balloon dilation

David J. Driscoll, Peter S. Hesslein, Charles E. Mullin

Baylor College of Medicine and the Texas Heart Institute.
United States

American Journal of Cardiology
Am J Cardiol 1982; 49: 1767-1772
DOI: 10.1016/0002-9149(82)90257-0

Abstract
Congenital stenosis of the pulmonary veins is a rare but frequently lethal congenital cardiac abnormality. Eight patients with this malformation were diagnosed, evaluated and treated. All eight patients had associated congenital cardiac defects. Two of the eight died, one of sepsis and one after operative pulmonary venoplasty. In three patients who underwent transvenous balloon catheter dilation of the stenosis the procedure provided immediate but transient relief of the stenosis. The prognosis for symptomatic infants with pulmonary vein stenosis is poor and its treatment an enigma.

Category
Stenosis or Obstruction of Normal Pulmonary Venous Connections
Length of Life Associated with Pulmonary Venous Obstruction
Catheter-mediated Interventions: Efficacy or Lack of Efficacy
Surgical Interventions for Pulmonary Venous Obstruction After the Onset of Disease

Year of Publication: 1982

Age Focus: Pediatric

Article Type: Case Reports or Retrospective Observations in Small Groups of Patients (≤10 patients)

Article Access: Free PDF File or Full Text Article Available Through PubMed or DOI: No