Shanta Chakrabarti, Ralph Mittal, James P. Gnanapragasam, Robin P. Martin
Bristol Royal Hospital for Children.
United Kingdom
Cardiology in the Young
Cardiol Young 2007; 17: 322-327
DOI: 10.1017/S1047951107000546
Abstract
Pulmonary venous stenosis has been a challenge to paediatric cardiologists and surgeons. In spite of significant improvements in the management and outcome of various congenital cardiac problems, the prognosis of this condition continues to be dismal. Acquired stenosis of the pulmonary veins has been described in the adult population, especially after radiofrequency ablation for atrial arrhythmias. The outcome of this condition has generally been described to be favourable in the long term. Acquisition of pulmonary venous stenosis in childhood has a very different outcome, and is not a very well recognised entity, with symptoms and signs which are non-specific. We present 7 infants who, when first assessed, had normal pulmonary veins, but who subsequently acquired stenoses of the veins, with very significant resultant morbidity and mortality.
Category
Stenosis or Obstruction of Normal Pulmonary Venous Connections
Patient Factors Influencing the Onset, Severity or Outcome of Disease
Length of Life Associated with Pulmonary Venous Obstruction
Year of Publication: 2007
Age Focus: Pediatric
Article Type: Case Reports or Retrospective Observations in Small Groups of Patients (≤10 patients)
Article Access: Free PDF File or Full Text Article Available Through PubMed or DOI: No