Cung-Van Cong, Tran-Thi Ly, Nguyen Minh Duc
National Lung Hospital. Pham Ngoc Thach University of Medicine.
Vietnam
Radiology Case Reports
Radiol Case Rep 2022; 17: 1313-1317
DOI: 10.1016/j.radcr.2022.01.057
Abstract
The unilateral absence of the pulmonary vein, known as pulmonary vein atresia, is a rare type of unilateral pulmonary venous hypoplasia caused by the congenital atrophy of the long pulmonary vein segments in one lung. The involved lung may be normal in size or present with hypoplasia and is often characterized by increased interstitial attenuation and interlobular septal thickening due to venous stasis, edema, and fibrosis. Pulmonary angiography often reveals a reduced size for the lateral pulmonary artery, peripherally sparse pulmonary vessels, contrast stasis, and the inability to visualize pulmonary veins. Symptoms include coughing up blood and infection. We present the clinical case of a patient who was initially diagnosed with recurrent hemoptysis due to pulmonary tuberculosis, followed by unsuccessful treatment. Imaging by 64-slice computed tomography with contrast injection using multiplanar reformation and volume rendering techniques allowed this case to be definitively diagnosed. This report emphasizes the epidemiological factors and clinical and imaging features of unilateral pulmonary vein atresia to prevent confusion and facilitate proper diagnosis in similar cases.
Category
Absence or Atresia of Normal Pulmonary Venous Connections
Symptoms and Quality of Life Associated with Pulmonary Venous Obstruction
Diagnostic Testing. Noninvasive
Year of Publication: 2022
Age Focus: Adult
Article Type: Case Reports or Retrospective Observations in Small Groups of Patients (≤10 patients). Article Type: Literature Review and Analysis.
Article Access: Free PDF File or Full Text Article Available Through PubMed or DOI: Yes