Unilateral pulmonary vein atresia without anomalous connection in adult patient with recurrent severe hemoptysis

Andrea Dell’Amore, Alessio Campisi, Stefano Congiu, Domenica Giunta, Giampiero Dolci, Fabio Niro

S. Orsola University Hospital.
Italy

Journal of Visualized Surgery
J Vis Surg 2018; 4:
DOI: 10.21037/jovs.2018.05.03

Abstract
Isolated unilateral pulmonary vein atresia (UPVA) is a rare congenital malformation and the management remains controversial. In adults, pneumonectomy is the treatment of choice when significant hemoptysis becomes life-threatening. We report a case of a 28-year-old male with isolated unilateral right atresia of the pulmonary vein who had life-threatening hemoptysis treated with bronchial arteries embolization followed by successful right pneumonectomy.

Category
Absence or Atresia of Normal Pulmonary Venous Connections
Symptoms and Quality of Life Associated with Pulmonary Venous Obstruction

Year of Publication: 2018

Age Focus: Adult

Article Type: Case Reports or Retrospective Observations in Small Groups of Patients (≤10 patients)

Article Access: Free PDF File or Full Text Article Available Through PubMed or DOI: Yes