Yan Wang, Shuangshuang Jiang, Jiasheng Yang, Ruilin Sun
Guangdong Second Provincial General Hospital.
China
Respiratory Medicine Case Reports
Respir Med Case Rep 2022;
DOI: 10.1016/j.rmcr.2022.101711
Abstract
UPVA (Unilateral pulmonary vein atresia) is the failure of connection between the common pulmonary vein and the left atrium. UPVA is a rare malformation of common pulmonary vein caused by embryonic development defects. Isolated UPVA is uncommon, the diagnosis commonly occurs during early childhood because of asthma, recurrent pneumonia or hemoptysis, but diagnosis in adults is unusual. Some patients can be asymptomatic until adulthood. In this report, we describe a case about UPVA presenting with recurrent hydrothorax in an adult. We gradually carried out routine diagnostic methods and eventually confirmed the rare UPVA according to the two common clinical manifestations of repeated pleural effusion and hilar soft tissue shadow.
Category
Absence or Atresia of Normal Pulmonary Venous Connections
Diagnostic Testing. Noninvasive
Symptoms and Quality of Life Associated with Pulmonary Venous Obstruction
Year of Publication: 2022
Age Focus: Pediatric or Adult
Article Type: Case Reports or Retrospective Observations in Small Groups of Patients (≤10 patients)
Article Access: Free PDF File or Full Text Article Available Through PubMed or DOI: Yes