Unilateral Pulmonary Vein Atresia Initially Presenting as Interstitial Lung Disease in an Elderly Female: Serial Chest Radiograph Changes and Its Literature Review

Young Woo Sim, Jongmin Park, Byunggeon Park, Jae-Kwang Lim, Kyung Min Shin, Young-Seon Kim

Yeungnam University Hospital and Yeungnam University College of Medicine. Kyungpook National University School of Medicine.
Republic of Korea

Journal of the Korean Society of Radiology
J Korean Soc Radiol 2022; 83: 372-377
DOI: 10.3348/jksr.2021.0033

Abstract
Unilateral pulmonary vein atresia (PVA) is a rare congenital cardiovascular anomaly occurring after the common pulmonary vein fails to incorporate into the left atrium. It is most commonly diagnosed in childhood, and diagnosis after reaching adulthood is extremely rare. Dyspnea on exertion and hemoptysis are common clinical features in adult PVA patients, whereas lung parenchymal abnormalities are indirect signs of PVA, which can manifest as interstitial lung disease. Herein, we present the case of a 62-year-old female diagnosed with unilateral PVA presenting as unilateral interstitial lung disease and report the changes in her chest radiographs over 12 years.

Category
Absence or Atresia of Normal Pulmonary Venous Connections
Diagnostic Testing. Noninvasive

Year of Publication: 2022

Age Focus: Adult

Article Type: Case Reports or Retrospective Observations in Small Groups of Patients (≤10 patients). Literature Review and Analysis.

Article Access: Free PDF File or Full Text Article Available Through PubMed or DOI: Yes