Mustafa Aparci, Murat Yalcin, Zafer Isilak, Mehmet Dogan and Ejder Kardesoglu
Haydarpasa Training Hospital, Mevki Military Hospital.
Turkey
Acta Cardiology Sinica
Acta Cardiol Sin 2016; 32: 758-761
DOI: 10.6515/acs20160129a
Abstract
Cor triatriatum sinister (CTS) is a rare congenital abnormality. Clinical presentation of patients with CTS mainly depends on the anatomic features of membrane and may vary from mild or moderate symptoms mimicking mitral stenosis to more severe and complicated cardioembolic stroke or a new onset heart failure. We herein have reported on a young male who presented with the signs and symptoms of mitral stenosis and was diagnosed as CTS with gradient on the orifice of the membrane after transthrocacic echocardiography. Computerized tomographic angiography revealed that the patient had unilateral, left sided pulmonary arterial hypoplasia and pulmonary vein atresia, with only the right pulmonary veins draining into the left atrial chamber. Further cardiac imaging by either computed tomography or magnetic resonance imaging is necessary in order to seek accompanying cardiac and vascular abnormalities. Patients with CTS have improved short and long term survival rates if CTS and accompanying abnormalities are surgically treated before the disease is complicated with heart failure, pulmonary hypertension, stroke and etc.
Category
Absence or Atresia of Normal Pulmonary Venous Connections
Symptoms and Quality of Life Associated with Pulmonary Venous Obstruction
Length of Life Associated with Pulmonary Venous Obstruction
Diagnostic Testing. Noninvasive
Year of Publication: 2016
Age Focus: Adult
Article Type: Case Reports or Retrospective Observations in Small Groups of Patients (≤10 patients)
Article Access: Free PDF File or Full Text Article Available Through PubMed or DOI: Yes