Savitri Shrivastava, James H . Moller, Jesse E . Edwards
University of Minnesota.
United States
Pediatric Cardiology
Pediatr Cardiol 1986; 7: 213-219
DOI: 10.1007/BF02093183
Abstract
A patient presenting with the rare association of congenital unilateral pulmonary venous atresia in one lung and pulmonary veno-occlusive disease in the other is described. The patient first presented at the age of 3 1/2 years with anemia, hemoptysis, and pulmonary hypertension. After cardiac catheterization and angiocardiography, a diagnosis of atresia of the left pulmonary veins was made for which left pneumonectomy was done. Four years later the patient presented with right-sided congestive failure and radiologic evidence of right-sided pulmonary edema from which death resulted. At autopsy, the right lung showed changes of pulmonary veno-occlusive disease, while the major veins were not involved.
Category
Absence or Atresia of Normal Pulmonary Venous Connections
Pulmonary Hypertension Associated with Stenosis or Atresia of Pulmonary Veins
Diagnostic Testing. Invasive
Surgical Interventions for Pulmonary Venous Obstruction After the Onset of Disease
Pulmonary Venous Pathology
Year of Publication: 1986
Age Focus: Pediatric
Article Type: Case Reports or Retrospective Observations in Small Groups of Patients (≤10 patients)
Article Access: Free PDF File or Full Text Article Available Through PubMed or DOI: No