Ryan Callahan, Brian H. Morray, Russel Hirsch, Christopher J. Petit
Boston Children’s Hospital and Harvard Medical School. Seattle Children’s Hospital and University of Washington School of Medicine. Cincinnati Children’s Hospital and University of Cincinnati College of Medicine. Morgan Stanley Children’s Hospital, NewYork-Presbyterian Hospital and Columbia University Vagelos College of Physicians and Surgeons.
United States
Journal for the Society for Cardiovascular Angiography and Interventions
J Soc Cardiovasc Angiogr Interv 2022;
DOI: 10.1016/j.jscai.2022.100391
Abstract
Pediatric intraluminal pulmonary vein stenosis has evolved into a chronic illness, with improving survival. Although significant knowledge gaps remain, medical providers have found success in the management of patients with pulmonary vein stenosis using a comprehensive multimodality treatment strategy. This review discusses the core principles employed by 4 centers dedicated to improving pulmonary vein stenosis outcomes, including how to make the diagnosis, educating the family, treatment strategy, the importance of surveillance, and the management of symptoms and comorbidities.
Category
Stenosis or Obstruction of Normal Pulmonary Venous Connections
Stenosis or Obstruction of Pulmonary Veins Following Surgical Repair of Anomalous Pulmonary Venous Connection
Pulmonary Hypertension Associated with Stenosis or Atresia of Pulmonary Veins
Symptoms and Quality of Life Associated with Pulmonary Venous Obstruction
Diagnostic Testing. Noninvasive
Diagnostic Testing. Invasive
Catheter-mediated Interventions: Efficacy or Lack of Efficacy
Medical Therapy to Prevent Progression of Disease. Efficacy or Lack of Efficacy
Medical Therapy to Prevent Recurrence of Disease after an Intervention. Efficacy or Lack of Efficacy
Medical Therapy for Pulmonary Hypertension Associated with Pulmonary Venous Obstruction. Efficacy or Lack of Efficacy
Year of Publication: 2022
Age Focus: Pediatric
Article Type: Review
Article Access: Free PDF File or Full Text Article Available Through PubMed or DOI: Yes