An Extremely Rare Variant of Pulmonary Venous Atresia

Yuki Nakamura, Kagami Miyaji, Yurie Miyata, Atsushi Kitagawa

Kitasato University Hospital.
Japan

Annals of Thoracic Surgery
AnnThorac Surg 2016; 101: 2382-2384
DOI: 10.1016/j.athoracsur.2015.08.085

Abstract
We describe an unusual case of a newborn with a rare variant of atresia of the common pulmonary vein that was mistaken for total anomalous pulmonary venous connection, cardiac type. The survival of patients with atresia of the common pulmonary vein is dependent on early diagnosis followed by immediate surgical repair, although early accurate diagnosis has been described as difficult in previous reports. Reverse aortic arch flow detected by echocardiography may be an important sign suggesting such a diagnosis.

Category
Absence or Atresia of Normal Pulmonary Venous Connections
Symptoms and Quality of Life Associated with Pulmonary Venous Obstruction
Diagnostic Testing. Noninvasive
Surgical Interventions for Pulmonary Venous Obstruction After the Onset of Disease
Length of Life Associated with Pulmonary Venous Obstruction

Year of Publication: 2016

Age Focus: Pediatric

Article Type: Case Reports or Retrospective Observations in Small Groups of Patients (≤10 patients)

Article Access: Free PDF File or Full Text Article Available Through PubMed or DOI: Yes