Absence or Atresia of Normal Pulmonary Venous Connections

Pediatric Pulmonary Vein Stenosis and Treatment

Joice Prodigios, Stephanie El Omeiri, Marcus Meneses, Bethelhem Belachew, Hansel J. Otero, David M. Biko, Jordan B. Rapp Children’s Hospital of Philadelphia and Perelman School of Medicine at The University of Pennsylvania.United States Seminars in RoentenologySemin Roentenol 2025; DOI: 10.1053/j.ro.2025.09.006 AbstractPulmonary vein stenosis (PVS) is an uncommon but often progressive condition in children, associated with high […]

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Mutations in VCP cause Adams-Oliver syndrome with or without pulmonary hypertension

Anna Lehman, Sana Ahmed, Arezoo Mohajeri, Alison M. Berezuk, Dhiraj Mannar, Spencer Cholak, Katharine S. Tuttle, James T. Bennett, Jeanine Aparecida Magno, Mark Hannibal, Gordana Kovacevik, Vladimir Kuburovic, M.E. Suzanne Lewis, Oana Moldovan, Zoe Nelson, Salmo Raskin, Anthony M. Vandersteen, Jared C. Roach, Sriram Subramaniam, Millan S. Patel University of British Columbia. University of Washington

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Commentary: Pulmonary vein stenosis: Not just a surgical solution

Harold M. Burkhart, Heather N. Anderson University of Oklahoma Health Sciences Center.United States Journal of Thoracic and Cardiovascular SurgeryJ Thorac Cardiovasc Surg 2021; DOI: 10.1016/j.jtcvs.2020.06.066 AbstractAbstract Not Available CategoryStenosis or Obstruction of Normal Pulmonary Venous ConnectionsAbsence or Atresia of Normal Pulmonary Venous ConnectionsStenosis or Obstruction of Pulmonary Veins Following Surgical Repair of Anomalous Pulmonary Venous Connections

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Prognostic Significance of Computed Tomography Findings in Pulmonary Vein Stenosis

Laureen Sena, Ryan Callahan, Lynn A. Sleeper, Rebecca S. Beroukhim UMass Memorial Children’s Medical Center and University of Massachusetts Medical School. Boston Children’s Hospital and Harvard Medical SchoolUnited States ChildrenChildren 2021; 8: DOI: 10.3390/children8050402 Abstract(1) Pulmonary vein stenosis (PVS) can be a severe, progressive disease with lung involvement. We aimed to characterize findings by computed tomography

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Outcome after repair of cor triatriatum

Selcen Yaroglu Kazanci, Sitaram Emani, Doff B. McElhinney Children’s Hospital Boston.United States American Journal of CardiologyAm J Cardiol 2012; 109: 412-416DOI: 10.1016/j.amjcard.2011.09.029 AbstractCor triatriatum represents <0.1% of all congenital cardiac malformations. Symptoms in patients with cor triatriatum are related to pulmonary venous obstruction and pressure loading of the right side of the heart. The aim of

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The role of surgical therapy for pulmonary vein atresia in childhood

Jeffrey Shuhaiber, Maliha Rehman, Kathy Jenkins, Francis Fynn-Thompson, Emile Bacha Cincinnati Childrens Hospital. Boston Children’s Hospital.United States Pediatric CardiologyPediatr Cardiol 2011; 32: 639-645DOI: 10.1007/s00246-011-9942-7 AbstractThe outcome for children with pulmonary vein atresia has been historically poor. This report describes clinical outcomes after surgical treatment of primary and secondary pulmonary vein atresia. All patients undergoing surgery for

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Congenital anomalies of the pulmonary veins

Saroja Bharati, Maurice Lev National Institutes of Health, National Heart and Lung InstituteUnited States Cardiovascular ClinicsCardiovasc Clin 1973; 5: 23-41DOI: Not Available AbstractAbstract Not Available CategoryStenosis or Obstruction of Normal Pulmonary Venous Connections Absence or Atresia of Normal Pulmonary Venous ConnectionsPulmonary Venous Pathology Year of Publication: 1973 Age Focus: Pediatric Article Type: Case Reports or

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Transcatheter Management of Pulmonary Vein Stenosis in Children

Connie Choi, Ryan Callahan Seattle Children’s Hospital. Children’s Hospital of Philadelphia.United States Pediatric CardiologyPediatr Cardiol 2025;DOI: 10.1007/s00246-025-04130-x AbstractPediatric intraluminal pulmonary vein stenosis (PVS) is a challenging condition where the diagnosis is confirmed via cardiac catheterization. The patient population is complex with inherent hemodynamic vulnerabilities, and the high rate of restenosis necessitates recurrent, technically demanding transcatheter interventions.

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A rare case of isolated unilateral pulmonary vein atresia presenting as interstitial lung disease in a young adult

Arnav Shandil, Mansi Verma, Sushma Makhaik, Sumala Kapila Indira Gandhi Medical CollegeIndia Journal of Cardiovascular and Thoracic ResearchJ Cardiovasc Thorac Res 2025; 17: 212-214DOI: 10.34172/jcvtr.025.33139 AbstractUnilateral pulmonary vein atresia is an unusual congenital cardiovascular abnormality. It occurs due to failure of incorporation of pulmonary veins into the left atrium. It is usually diagnosed in childhood and

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Anomalies of Pulmonary Circulation as a Cause of Hemoptysis: A Series of Unusual Cases and Review of the Literature

Kamini Gupta, Kavita Saggar, Amit Goyal, Avik Banerjee Dayanand Medical College and Hospital.India Oman Medical JournalOman Med J 2015; 30: 208-211DOI: 10.5001/omj.2015.43 AbstractThe expectoration of blood originating from the lower respiratory tract, called hemoptysis, is a common clinical condition with many potential etiologies. Massive hemoptysis is life threatening and needs urgent intervention. Multidetector computed tomography (MDCT)

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