Article Type: Case Reports or Retrospective Observations in Small Groups of Patients (≤10 patients)

Pulmonary vein stenosis with Down syndrome: a rare and frequently fatal cause of pulmonary hypertension in infants and children

Srinath Gowda, Deepti Bhat, Zhuang Feng, Chung-Ho Chang, Robert D. Ross The Children’s Hospital of Michigan and Detroit Medical Center.United States Congenital Heart DiseaseCongenit Heart Dis 2014; 9: E90-E97DOI: 10.1111/chd.12088 AbstractDown syndrome (DS) patients are prone to pulmonary hypertension (PHTN) due to various cardiopulmonary causes. However, the association of DS with pulmonary vein stenosis (PVS) is […]

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An infant with primary pulmonary vein stenosis, associated with fatal occlusion of intraparenchymal small pulmonary veins

Takanari Fujii, Hideshi Tomita, Hiroaki Kise, Kazuto Fujimoto, Kozue Kobayashi, Yoshitaka Watanabe, Takeshi Yamazaki, Takeshi Shimizu, Shunsuke Sakurai, Satoshi Hibino, Junya Iwasaki, Takashi Soga, Shigeru Uemura, Kazuo Itabashi, Shigeo Yamaki Showa University Northern Yokohama Hospital. Japanese Research Institute of Pulmonary Vasculature.Japan Journal of Cardiology CasesJ Cardiol Cases 2013; 9: 3-7DOI: 10.1016/j.jccase.2013.08.013 AbstractPrimary pulmonary vein stenosis (PVS)

An infant with primary pulmonary vein stenosis, associated with fatal occlusion of intraparenchymal small pulmonary veins Read More »

Technique of coronary sinus plasty for left pulmonary vein stenosis

David Kalfa, Wyman Lai, Anne Ferris, Usha Krishnan, Emile Bacha Morgan Stanley Children’s Hospital of New York and Columbia University.United States Annals of Thoracic SurgeryAnn Thorac Surg 2014; 98: e27-e29DOI: 10.1016/j.athoracsur.2014.03.045 AbstractWe describe a technique of coronary sinus plasty used to treat an infant with compression of the left pulmonary vein between the descending aorta and

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Hemoptysis from bronchial varices associated with pulmonary vein stenosis: role of surgical repair

A. Walsh, G. Canny, C.J. McMahon, J. M. Redmond, P. McNally Our Lady’s Children’s Hospital.Ireland Pediatric PulmonologyPediatr Pulmonol 2013; 48: 838-840DOI: 10.1002/ppul.22659 AbstractWe present the case of a 6-year-old child who presented with an episode of life threatening hemoptysis. Investigations revealed multiple areas of endobronchial varices and abnormal pleural vessels as well as severe left pulmonary

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Abnormalities in embryological development in total anomalous pulmonary venous connection. A case report

Mihaela Balgradean, Eliza Cinteza, C. Cirstoveanu, Augustina Enculescu, Doina Plesca “Marie Skĺodowska-Curie” Emergency Children’s Hospital.Romania Romanian Journal of Morphology and EmbryologyRom J Morphol Embryol 2013; 54: 635-637DOI: Not Available AbstractPulmonary venous system development starts early in embryonic life. Abnormalities in the development of pulmonary venous system occur either by the absence of common pulmonary vein

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Pulmonary vein stenosis: expression of receptor tyrosine kinases by lesional cells

Wolfram F. J. Riedlinger, Amy L. Juraszek, Kathy J. Jenkins, Alan W. Nugent, Sowmya Balasubramanian, Monica L. Calicchio, Mark W. Kieran, Tucker Collins Children’s Hospital Boston and Harvard Medical School.United States Cardiovascular PathologyCardiovasc Pathol 2006; 15: 91-99DOI: 10.1016/j.carpath.2005.11.006 AbstractBackground: Primary pulmonary vein stenosis (PVS) is a progressive disorder of infants. Although catheter based intervention and chemotherapy are

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Pulmonary vein atresia with severe contralateral pulmonary vein stenosis in a child

Jeffrey E. Vergales, Shawn C. West, Andrew W. Hoyer University of Virginia Health SystemUnited States Pediatric CardiologyPediatr Cardiol 2012; 33: 663-665DOI: 10.1007/s00246-012-0178-y AbstractUnilateral pulmonary vein atresia is a very rare congenital anomaly associated with high morbidity and mortality. Most cases present in infancy or childhood with recurrent respiratory infections or hemoptysis. Further, the diagnosis can often

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Serum Levels After Everolimus-Stent Implantation and Paclitaxel-Balloon Angioplasty in an Infant with Recurrent Pulmonary Vein Obstruction After Repaired Total Anomalous Pulmonary Venous Connection

Matthias J. Muller, Ulrich Krause, Thomas Paul, Heike E. Schneider Georg-August-University Göttingen.Germany Pediatric CardiologyPediatr Cardiol 2011; 32: 1036-1039DOI: 10.1007/s00246-011-0054-1 AbstractEverolimus-eluting stents and paclitaxel-coated balloons are used in the interventional treatment of coronary artery disease in adults to reduce the restenosis rate and in small-vessel disease. Both substances are released into the circulation. We report systemic drug

Serum Levels After Everolimus-Stent Implantation and Paclitaxel-Balloon Angioplasty in an Infant with Recurrent Pulmonary Vein Obstruction After Repaired Total Anomalous Pulmonary Venous Connection Read More »

Cardiopulmonary magnetic resonance imaging in children after lung transplantation: preliminary observations

Lars Grosse-Wortmann, Shi-Joon Yoo, Melinda Solomon, Christopher K. Macgowan, Shaf Keshavjee, Hartmut Grasemann Hospital for Sick Children and University of Toronto.Canada Journal of Heart and Lung TransplantationJ Heart Lung Transplant 2011; 30: 1294-1298DOI: 10.1016/j.healun.2011.07.008 AbstractBackground: Lung transplantation carries a guarded prognosis and is burdened by short-term and long-term complications that affect the airway, lungs, and vasculature. In

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Hypoplastic right lung associated with right pulmonary vein stenosis and systemic collateral

Anant Khositseth, Suvipaporn Siriporpitak, Preecha Laohakunakorn Ramathibodi Hospital Mahidol University.Thailand Congenital Heart DiseaseCongenit Heart Dis 2010; 5: 76-80DOI: 10.1111/j.1747-0803.2009.00324.x AbstractWe present a case of a 6-month-old girl diagnosed as unilateral pulmonary vein stenosis (right inferior pulmonary vein) with dextroposition of the heart, hypoplastic right lung, hypoplastic right pulmonary artery, collateral from the descending aorta supplied right

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