Diagnostic Testing. Invasive

Silent unilateral pulmonary venous obstruction. Occurrence after surgical correction of transposition of the great arteries

James E. Lock, Russell V. Lucas, Kurt Amplatz, F. Blanton Bessinger Jr.University of MinnesotaUnited States ChestChest 1978; 73: 224-227DOI:https://doi.org/10.1378/chest.73.2.224 AbstractAn 11-year-old girl was found to have completely obstructed left pulmonary veins eight years following corrective surgery for transposition of the great arteries. The patient was acyanotic and asymptomatic. Retrograde flow of arterial blood from the […]

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The impact of right ventricular pressure and function on survival in patients with pulmonary vein stenosis

Michelle C. Sykes, Christina Ireland, Julia E. McSweeney, Emily Rosenholm, Kristofer G. Andren, Thomas J. Kulik Boston Children’s Hospital.United States Pulmonary CirculationPulm Circ 2018;DOI: 10.1177/2045894018776894 AbstractPulmonary vein stenosis (PVS) is associated with pulmonary hypertension (PH), but there is little information regarding the impact of PH on right ventricular (RV) systolic function and survival. We conducted a

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Intraluminal Pulmonary Vein Stenosis in Children: A “New” Lesion

Viviane G. Nasr, Ryan Callahan, Zachary Wichner, Kirsten C. Odegard, James A. DiNardo Boston Children’s Hospital.United States Anesthesia and AnalgesiaAnesth Analges 2019; 129: 27-40DOI: 10.1213/ANE.0000000000003924 AbstractPulmonary vein stenosis (PVS) is a rare disorder that leads to progressive narrowing of the extrapulmonary veins. PVS has been reported in both children and adults and in its worse iteration

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Management of Complex Pulmonary Vein Stenosis at Altitude Combining Comprehensive Percutaneous Interventional Treatment with Sirolimus, Pulmonary Hypertension Medications and Intraluminal Imaging with Optical Coherence Tomography

Michael J. Shorofsky, Gareth J. Morgan, Ernesto Mejia, Salvador A. Rodriguez, Megan Greene, Paige Sheaks, Dunbar Ivy, Jenny E. Zablah University of Colorado and Children’s Hospital Colorado.United States Pediatric CardiologyPediatr Cardiol 2023; Online ahead of printDOI: 10.1007/s00246-023-03102-3 AbstractBackground: Pulmonary vein stenosis (PVS) is a growing problem for the pediatric congenital heart population. Sirolimus has previously been shown

Management of Complex Pulmonary Vein Stenosis at Altitude Combining Comprehensive Percutaneous Interventional Treatment with Sirolimus, Pulmonary Hypertension Medications and Intraluminal Imaging with Optical Coherence Tomography Read More »

Acute Pulmonary Vasodilator Testing and Long-Term Clinical Course in Segmental Pulmonary Vascular Disease

Liezl Domingo, H. Sonali Magdo, Ronald W. Day University of Utah and Primary Children’s Hospital.United States Pediatric CardiologyPediatr Cardiol 2018; 39: 501-508DOI: 10.1007/s00246-017-1780-9 AbstractResults of acute pulmonary vasodilator testing (AVT) and the outcome of medical therapy have not been described in patients with segmental pulmonary vascular disease (SPVD). We sought to compare the pulmonary vasodilatory effects

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Doppler Echocardiographic Features of Pulmonary Vein Stenosis in Ex-Preterm Children

Yalin Lin, Alena K. Amin, Roberta L. Keller, David F. Teitel, Hythem M. Nawaytou University of California, San Francisco.United States Journal of the American Society of EchocardiographyJ Am Soc Echocardiogr 2022; 35: 435-442DOI: 10.1016/j.echo.2021.12.015 AbstractBackground: Echocardiography is used to screen for the presence of pulmonary vein stenosis (PVS) in ex-preterm infants and children. However, there are no

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Correlation of Intravascular Ultrasound with Histology in Pediatric Pulmonary Vein Stenosis

Ryan Callahan, Zachary Gauthier, Shuhei Toba, Stephen P. Sanders, Diego Porras, Sara O. Vargas Boston Children’s Hospital and Harvard Medical School.United States ChildrenChildren 2021; 8DOI: 10.3390/children8030193 AbstractPreliminary intravascular ultrasound (IVUS) images of suspected pediatric intraluminal pulmonary vein stenosis (PVS) demonstrate wall thickening. It is unclear how the IVUS-delineated constituents of wall thickening correlate with the histology.

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Preliminary findings on the use of intravascular ultrasound in the assessment of pediatric pulmonary vein stenosis

Ryan Callahan, Kathy J. Jenkins, Zachary Gauthier, Kimberlee Gauvreau, Diego Porras Boston Children’s Hospital and Harvard Medical SchoolUnited States Catheterization and Cardiovascular InterventionsCatheter Cardiovasc Interv 2021; 97: E362-E370DOI: 10.1002/ccd.29264 AbstractObjective: Determine the feasibility of performing intravascular ultrasound (IVUS) in pediatric pulmonary vein stenosis (PVS) and investigate whether IVUS can delineate the mechanism of PVS.Background: The use of IVUS

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Intravascular Ultrasound for Pulmonary Vein Stenosis Interventions in Congenital Heart Disease

Samantha A. Kops, Danielle Strah, Kwan S. Lee, Michael D. Seckeler University of Arizona.United States Journal of Invasive CardiologyJ Invasive Cardiol 2021; 33: E259-E262DOI: 10.25270/jic/20.00445 AbstractObjective: Pulmonary vein stenosis (PVS) is aggressive, with high morbidity and mortality. Surgical and catheter interventions yield modest success, at best. Refinements in catheter interventions could potentially improve outcomes in this patient

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Diagnostic performance of CT angiography to detect pulmonary vein stenosis in children

Christian A. Barrera, David Saul, Jordan B. Rapp, Christopher L. Smith, Ammie M. White, David M. Biko, Hansel J. Otero The Children’s Hospital of Philadelphia and University of Pennsylvania.United States International Journal of Cardiovascular ImagingInt J Cardiovasc Imaging 2020; 36: 141-147DOI: 10.1007/s10554-019-01693-8 AbstractTo assess the diagnostic efficiency of CT angiography (CTA) to detect pulmonary vein stenosis

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