Length of Life Associated with Pulmonary Venous Obstruction

Impact of Structured Surveillance and Intervention on Long-Term Vein Outcomes in Pediatric Pulmonary Vein Stenosis

Ashish Saini, Andrew Jergel, Yijin Xiang, Rosemary Gray, Dennis W. Kim, James A. Kuo Children’s Healthcare of Atlanta and Emory University School of Medicine.United States ChildrenChildren 2026; DOI: 10.3390/children13070933 AbstractBackground: Pediatric pulmonary vein stenosis (PVS) is a progressive and recurrent condition associated with high morbidity and mortality. Long-term outcomes of individual pulmonary veins remain poorly described. Methods: All pediatric […]

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Pulmonary Venous Decompressing Collaterals: Angiographic Characteristics and Impact on Outcomes in Pediatric Pulmonary Vein Stenosis

Ashish Saini, Hui Huang, Andrew Jergel, Rosemary Gray, Dennis W. Kim, James Kuo Children’s Healthcare of Atlanta and Emory University School of Medicine.United States Pediatric CardiologyPediatr Cardiol 2026;DOI: 10.1007/s00246-026-04350-9 AbstractPediatric pulmonary vein stenosis (PVS) is a rare, progressive condition associated with significant morbidity and mortality. While pulmonary venous decompressing collaterals (PVDC) have been described, their clinical

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Extracorporeal Membrane Oxygenation in Pediatric Pulmonary Hypertension: A Single-Center Cohort to Inform Decision-Making

Taylor M. Smith, Kathryn Restaino, Stuart Lipsitz, Jai Krishan Khurana, Mary P. Mullin, John N. Kheir, Katie M. Moynihan Boston Children’s Hospital, Brigham and Women’s Hospital and Harvard Medical School.United States American Society of Artificial Internal Organs JournalASAIO J 2026;DOI: 10.1097/MAT.0000000000002766 AbstractLimited data describe children with pulmonary hypertension (PH) supported on extracorporeal membrane oxygenation (ECMO). This

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Characteristics and outcomes of preterm infants with pulmonary vein stenosis in the contemporary era: a PHIS database analysis

Mohamed F. Elsisy, Fred Z. Lam, Mark M. Naguib, Mary E. Dees, James C. Gay, George T. Nicholson Monroe Carell Jr. Children’s Hospital at Vanderbilt. United States Journal of PerinatologyJ Perinatol 2026; DOI: 10.1038/s41372-026-02703-z AbstractBackground: Pulmonary vein stenosis (PVS) is increasingly recognized in preterm infants, yet data regarding characteristics and outcomes remain limited.Methods: A review of hospitalizations from

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Long-term outcomes of individualised repair in patients with primary pulmonary vein stenosis

Zhangwei Wang, Yang Yang Beijing Children’s Hospital, National Children’s Medical Center and Capital Medical University.China Cardiology in the YoungCardiol Young 2025; DOI: 10.1017/S1047951124026180 AbstractObjectives: Primary pulmonary vein stenosis is a rare congenital heart condition and carries a poor prognosis. Various surgical techniques have been introduced to treat primary pulmonary vein stenosis. However, there is no consensus on

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A New Variant in the GATA6 Gene Associated with Tracheoesophageal Fistula, Pulmonary Vein Stenosis, and Neonatal Diabetes

Flaminia Pugnaloni, Ludovica Martini, Domenico Umberto De Rose, Francesca Landolfo, Paola Giliberti, Rosario Ruta, Antonio Novelli, Novella Rapini, Fabrizio Barbetti, Alessandra Toscano, Andrea Conforti, Pietro Bagolan, Irma Capolupo, Andrea Dotta “Bambino Gesù” Children’s Hospital Istituto di Ricovero e Cura a Carattere Scientifico. University of Rome “Tor Vergata”. Italy Hormone Research in PaediatricsHorm Res Paediatr 2025;

A New Variant in the GATA6 Gene Associated with Tracheoesophageal Fistula, Pulmonary Vein Stenosis, and Neonatal Diabetes Read More »

Tricuspid Valve Blood Cysts Mimicking Thrombus or Vegetation on Echocardiogram in a Neonate

Takato Yamasaki, Rebecca Beroukhim, Stephen Sanders, Chrystalle Katte Carreon Boston Children’s Hospital and Harvard Medical School. Mie University Graduate School of Medicine. United States and Japan Pediatric CardiologyPediatr Cardiol 2023; 44: 245-248DOI: 10.1007/s00246-022-02978-x AbstractA 2-month-old male infant, born premature with a birth weight of 865 g, was found to have a tricuspid valve mass mimicking thrombus

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Single-institution outcomes of surgical repair of infracardiac total anomalous pulmonary venous connection

Guocheng Shi, Fang Zhu, Chen Wen, Lisheng Qiu, Haibo Zhang, Zhongqun Zhu, Huiwen Chen Shanghai Children’s Medical Center and Shanghai Jiao Tong University School of Medicine. China Journal of Thoracic and Cardiovascular SurgeryJ Thorac Cardiovasc Surg 2021; 161: 1408-1417DOI: 10.1016/j.jtcvs.2020.06.023 AbstractObjective: This contemporary study sought to describe the outcomes of patients undergoing biventricular repair of infracardiac total

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Midterm results and risk factors of functional single ventricles with extracardiac total anomalous pulmonary venous connection

Mikio Sugano, Masaya Murata, Yujiro Ide, Hiroki Ito, Kazuyoshi Kanno, Kenta Imai, Motonori Ishidou, Ryohei Fukuba, Kisaburou Sakamoto Mt. Fuji Shizuoka Children’s Hospital. Japan General Thoracic and Cardiovascular SurgeryGen Thorac Cardiovasc Surg 2019; 67: 941-948DOI: 10.1007/s11748-019-01141-3 AbstractObjectives: To evaluate the clinical outcomes of surgical repair of an extracardiac total anomalous pulmonary venous connection (TAPVC) in a functional

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Down Syndrome with Complete Atrioventricular Septal Defect, Hypertrophic Cardiomyopathy, and Pulmonary Vein Stenosis

Guruprasad Mahadevaiah, Manoj Gupta, Ravi Ashwath Rainbow Babies and Children’s Hospital.United States Texas Heart Institute JournalTex Heart Inst J 2015; 42: 458-461DOI: 10.14503/THIJ-14-4256 AbstractThe prevalence of congenital heart disease in infants with Down syndrome is 40%, compared with 0.3% in children who have normal chromosomes. Atrioventricular and ventricular septal defects are often associated with chromosomal aberrations,

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