Medical Therapy for Pulmonary Hypertension Associated with Pulmonary Venous Obstruction: Efficacy or Lackk of Efficacy

De Novo and Progressive Pulmonary Vein Stenosis Following Pediatric Heart Transplantation: A Multicenter Retrospective Study

Arene Butto, Conor O’Halloran, James Kuo, Anna Joong, Amanda L. Hauck, Alan Nugent, William Mahle, Paul Tannous Children’s Healthcare of Atlanta. Lurie Children’s Hospital.United States Pediatric TransplantationPediatr Transplant 2024; 28:DOI: 10.1111/petr.14828 AbstractBackground: Pulmonary vein stenosis (PVS) is a rare condition in which neointimal proliferation leads to venous and arterial hypertension. Little is known about PVS after heart […]

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Never Say Never: The Use of Nitric Oxide in Patients With Obstructed Pulmonary Veins: A Case Report

Victoria Sokoliuk, James A. DiNardo, Morgan L. Brown Boston Children’s Hospital.United States A and A PracticeA A Pract 2019; 12: 205-207DOI: 10.1213/XAA.0000000000000885 AbstractPulmonary vein stenosis (PVS) is a progressive disease with pulmonary hypertension (PH) as a major cause of morbidity and mortality. Traditional management of PH with inhaled nitric oxide (iNO) is typically avoided in PVS

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Management of Complex Pulmonary Vein Stenosis at Altitude Combining Comprehensive Percutaneous Interventional Treatment with Sirolimus, Pulmonary Hypertension Medications and Intraluminal Imaging with Optical Coherence Tomography

Michael J. Shorofsky, Gareth J. Morgan, Ernesto Mejia, Salvador A. Rodriguez, Megan Greene, Paige Sheaks, Dunbar Ivy, Jenny E. Zablah University of Colorado and Children’s Hospital Colorado.United States Pediatric CardiologyPediatr Cardiol 2023; Online ahead of printDOI: 10.1007/s00246-023-03102-3 AbstractBackground: Pulmonary vein stenosis (PVS) is a growing problem for the pediatric congenital heart population. Sirolimus has previously been shown

Management of Complex Pulmonary Vein Stenosis at Altitude Combining Comprehensive Percutaneous Interventional Treatment with Sirolimus, Pulmonary Hypertension Medications and Intraluminal Imaging with Optical Coherence Tomography Read More »

Acute Pulmonary Vasodilator Testing and Long-Term Clinical Course in Segmental Pulmonary Vascular Disease

Liezl Domingo, H. Sonali Magdo, Ronald W. Day University of Utah and Primary Children’s Hospital.United States Pediatric CardiologyPediatr Cardiol 2018; 39: 501-508DOI: 10.1007/s00246-017-1780-9 AbstractResults of acute pulmonary vasodilator testing (AVT) and the outcome of medical therapy have not been described in patients with segmental pulmonary vascular disease (SPVD). We sought to compare the pulmonary vasodilatory effects

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Intervening with the Nitric Oxide Pathway to Alleviate Pulmonary Hypertension in Pulmonary Vein Stenosis

Richard W. B. van Duin, Kelly Stam, André Uitterdijk, Beatrijs Bartelds, A. H. Jan Danser, Irwin K. M. Reiss, Dirk J. Duncker, Daphne Merkus Erasmus MC Rotterdam. Sophia Children’s Hospital. University Hospital, LMU Munich.Netherlands and Germany Journal of Clinical MedicineJ Clin Med 2019; 8DOI: 10.3390/jcm8081204 AbstractPulmonary hypertension (PH) as a result of pulmonary vein stenosis (PVS)

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Pulmonary Hypertension in the Preterm Infant with Chronic Lung Disease can be Caused by Pulmonary Vein Stenosis: A Must-Know Entity

Daniela Laux, Marie-Amelie Rocchisani, Younes Boudjemline, Marielle Gouton, Damien Bonnet, Caroline Ovaert Centre de Référence Malformations Cardiaques Congénitales Complexes-M3C-CCML, Centre Chirurgical Marie Lannelongue. Hôpital La Timone- Enfants.France Pediatric CardiologyPediatr Cardiol 2016; 7(2):313-321DOI: 10.1007/s00246-015-1279-1 AbstractPulmonary hypertension (PHT) in the preterm infant is frequently due to chronic lung disease. Rarely, PHT can be caused by pulmonary vein (PV)

Pulmonary Hypertension in the Preterm Infant with Chronic Lung Disease can be Caused by Pulmonary Vein Stenosis: A Must-Know Entity Read More »