Medical Therapy to Prevent Progression of Disease. Efficacy or Lack of Efficacy

Combination Chemotherapy in Severe Pulmonary Vein Stenosis-A Case Series

Gabriel Krivenko, Karen Iacono, David Nykanen, Robyn Keen, Robert Sutphin, Michael Farias University of Central Florida. Orlando Health Arnold Palmer Hospital for Children. Boston Children’s Hospital.United States ChildrenChildren 2023; 10: DOI: 10.3390/children10020364 AbstractPulmonary vein stenosis results from a proliferative process that leads to the progressive obstruction of venous return to the left atrium. It is often […]

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Pulmonary Vein Stenosis Associated with Germline PIK3CA Mutation

Delphine Yung, Kaitlyn Freeman, Ghayda Mirzaa University of Washington School of Medicine and Seattle Children’s Research Institute. Brotman Baty Institute for Precision Medicine.United States ChildrenChildren 2022; 9: DOI: 10.3390/children9050671 AbstractPulmonary vein stenosis is a rare and frequently lethal childhood disease. There are few known genetic associations, and the pathophysiology is not well known. Current treatments include

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New Paradigms for Pulmonary Vein Stenosis Treatment: When Surgery and Transcatheter Therapy Aren’t Good Enough

Usama B. Kanaan, William T. Mahle Children’s Healthcare of Atlanta and Emory University School of Medicine.United States Journal of PediatricsJ Pediatr 2018; 198: 12-13DOI: 10.1016/j.jpeds.2018.01.082 AbstractAbstract Not Available CategoryStenosis or Obstruction of Normal Pulmonary Venous ConnectionsStenosis or Obstruction of Pulmonary Veins Following Surgical Repair of Anomalous Pulmonary Venous ConnectionsMultidisciplinary CareMedical Therapy to Prevent or Reverse the

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Management of Pediatric Pulmonary Vein Stenosis

Ryan Callahan, Brian H. Morray, Russel Hirsch, Christopher J. Petit Boston Children’s Hospital and Harvard Medical School. Seattle Children’s Hospital and University of Washington School of Medicine. Cincinnati Children’s Hospital and University of Cincinnati College of Medicine. Morgan Stanley Children’s Hospital, NewYork-Presbyterian Hospital and Columbia University Vagelos College of Physicians and Surgeons.United States Journal for

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Evaluation of Treatment Effect of Sirolimus on Pediatric Pulmonary Vein Stenosis Using a Neonatal Rat Model Induced by Bilateral Pulmonary Vein Banding

Kathy J. Jenkins Boston Children’s Hospital and Harvard Medical School.United States Journal of the American College of Cardiology Basic Translational ScienceJACC Basic Transl Sci 2025; 10: DOI: 10.1016/j.jacbts.2025.04.010 AbstractAbstract Not Available CategoryStenosis or Obstruction of Normal Pulmonary Venous ConnectionsPulmonary Hypertension Associated with Stenosis or Atresia of Pulmonary VeinsPulmonary Venous PathologyMedical Therapy to Prevent or Reverse the

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Evaluation of Treatment Effect of Sirolimus on Pediatric Pulmonary Vein Stenosis Using a Neonatal Rat Model

Debao Li, Yingying Xiao, Peisen Ruan, Zunmin Wan, Yuqing Hu, Sijuan Sun, Zheng Wang, Sixie Zheng, Yi Yan, Hao Chen, Hao Zhang, Chun Shen, Qi Sun, Lincai Ye Shanghai Children’s Medical Center and Shanghai Jiao Tong University School of Medicine. Children’s Hospital of Fudan University and National Children’s Medical Center. Women and Children’s Hospital of

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Valsartan to Prevent Acquired Pulmonary Vein Stenosis in Pediatric Patients After Total Anomalous Pulmonary Venous Connection Surgery

Jin Shentu, Mingjie Zhang, Zhuoming Xu, Chen Wen, Hao Zhang, Zhongqun Zhu, Huiwen Chen, Guocheng Shi Shanghai Children’s Medical Center and Shanghai Jiao Tong University.China Journal of the American Heart AssociationJ Am Heart Assoc 2025; 14:DOI: 10.1161/JAHA.124.036911 AbstractBackground: Recurrent pulmonary vein stenosis (PVS) following surgical repair of total anomalous pulmonary venous connection is associated with poor prognosis. Preclinical studies have shown that use of an angiotensin receptor blocker can attenuate intimal hyperplasia;

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Targeted Rapamycin Delivery via Magnetic Nanoparticles to Address Stenosis in a 3D Bioprinted in Vitro Model of Pulmonary Veins

Liqun Ning, Stefano Zanella, Martin M. Tomov, Medhi Salar Amoli, Linqi Jin, Bouen Hwang, Maher Saadeh, Huang Chen, Sunder Neelakantan, Lakshmi Prasad Dasi, Reza Avazmohammadi, Morteza Mahmooudi, Holly D. Bauser-Heaton, Vahid Serpooshan Emory University School of Medicine, Children’s Healthcare of Atlanta and Georgia Institute of Technology. Cleveland State University. Texas A&M University. Michigan State University.United

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In Search of the Holy Grail for Pediatric Pulmonary Vein Stenosis

Lourdes R. Prieto Nicklaus Children’s Hospital.United States Journal of the American College of CardiologyJ Am Coll Cardiol 2021; 77: 2819-2821DOI: 10.1016/j.jacc.2021.04.029 AbstractAbstract Not Available CategoryMedical Therapy to Prevent or Reverse the Onset of Disease. Efficacy or Lack of EfficacyMedical Therapy to Prevent Progression of Disease. Efficacy or Lack of EfficacyMedical Therapy to Prevent Recurrence of Disease

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Commentary: Targeting neointimal lesions in pulmonary vein stenosis: Fact or fiction?

Rachel D. Vanderlaan Hospital for Sick Children.Canada Journal of Thoracic and Cardiovascular SurgeryJ Thorac Cardiovasc Surg 2020; 160: 794-795DOI: 10.1016/j.jtcvs.2020.02.021 AbstractAbstract Not Available CategoryStenosis or Obstruction of Normal Pulmonary Venous ConnectionsStenosis or Obstruction of Pulmonary Veins Following Surgical Repair of Anomalous Pulmonary Venous ConnectionsMedical Therapy to Prevent or Reverse the Onset of Disease. Efficacy or Lack

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