Patient Factors Influencing the Onset, Severity or Outcome of Disease

Infantile form of scimitar syndrome with contralateral pulmonary vein stenosis

I. Ricardo Argueta-Morales, Lauren C. Meador, David G. Nykanen, William M. DeCampli Arnold Palmer Hospital for Children.United States Pediatric CardiologyPediatr Cardiol 2010; 31: 550-552DOI: 10.1007/s00246-009-9630-z AbstractInfantile scimitar syndrome (SS) carries significant mortality. Consistent management guidelines have not been well established, and outcomes continue to be disappointing. We present our experience managing an SS patient with complex […]

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A mother and daughter with the p.R443X mutation of mucopolysaccharidosis type II: Genotype and phenotype analysis

Young Bae Sohn, Su Jin Kim, Sung Won Park, Hyung-Doo Park, Chang-Seok Ki, Chi Hwa Kim, Seung Won Huh, Sunghee Yeau, Kyung-Hoon Paik, Dong-Kyu Jin Samsung Medical Center.Republic of Korea American Journal of Medical GeneticsAm J Med Genet 2010; 152A: 3129-3132DOI: 10.1002/ajmg.a.33589 AbstractMucopolysaccharidosis type II (Hunter syndrome) is a lysosomal storage disease caused by a deficiency

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Outcomes and Risk Factors of Interventions for Pediatric Post-operative Pulmonary Vein Stenosis

Kristin T. Fujita, Michael P. DiLorenzo, Usha Krishnan, Mariel E. Turner, Oliver M. Barry, Alejandro J. Torres, Emile A. Bacha, David Kalfa, Matthew A. Crystal Columbia University Vagelos College of Physicians and Surgeons and New York-Presbyterian.United States Pediatric CardiologyPediatr Cardiol 2023;DOI: 10.1007/s00246-023-03214-w AbstractPulmonary vein stenosis (PVS) in children is a challenging condition with poor outcomes. Post-operative

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Management of pulmonary venous obstruction after correction of TAPVC: risk factors for adverse outcome

Marco Ricci, M. Elliotta, G. A. Cohen, G. Catalana, J. Stark, Mark R. de Leval, V. T. Tsang Great Ormond Street Hospital for Children NHS Trust.United Kingdom European Journal of Cardiothoracic SurgeryEur J Cardiothorac Surg 2003; 24: 28-36DOI: 10.1016/s1010-7940(03)00180-5 AbstractObjective: Recurrent pulmonary venous obstruction (PVO) occurs in 0-18% of infants undergoing correction of total anomalous pulmonary venous

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Pulmonary vein stenosis in heart transplant patients

Connie Choi, Brian H. Morray, Humera Ahmed, Mariska Kemna Seattle Children’s Hospital.United States Pediatric TransplantationPediatr Transplant 2023;DOI: 10.1111/petr.14636 AbstractBackground: Pulmonary vein stenosis (PVS) is a rare pediatric condition associated with significant mortality and morbidity. PVS in patients following heart transplant (HT) has not yet been described.Methods: Patients who had clinically significant PVS following a heart transplant during the

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Acquired left-sided pulmonary vein stenosis in an extremely premature infant: a new entity?

John T. Benjamin, Charles R. Hamm, Michael Zayek, Fabien G. Eyal, Steve Carlson, Elizabeth Manci University of South Alabama.United States Journal of PediatricsJ Pediatr 2009; 54: 459DOI: 10.1016/j.jpeds.2008.08.022 AbstractNo Abstract Available CategoryStenosis or Obstruction of Normal Pulmonary Venous ConnectionsPatient Factors Influencing the Onset, Severity or Outcome of Disease Year of Publication: 2009 Age Focus: Pediatric Article

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The recent surgical result of total anomalous pulmonary venous return

So-Ick Jang, Jin-Young Song, Soo-Jin Kim, Eun Young Choi, Woo Sup Shim, Chul Lee, Hong-Gook Lim, Chang Ha Lee Sejong General Hospital.Republic of Korea Korean Circulation JournalKorean Circ J 2010; 40: 31-35DOI: 10.4070/kcj.2010.40.1.31 AbstractBackground and objectives: Recent surgical results from total anomalous pulmonary venous return (TAPVR) are reported to have improved; however, mortality and morbidity are still

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Pulmonary vein stenosis: prematurity and associated conditions

David M. Drossner, Dennis W. Kim, Kevin O. Maher, William T. Mahle Emory University School of Medicine.United States PediatricsPediatrics 2008; 122: e656-e661DOI: 10.1542/peds.2008-0075 AbstractObjective: Pulmonary vein stenosis is a rare, although often lethal, anomaly. Risk factors for the diagnosis of pulmonary vein stenosis are poorly characterized. In this study we sought to identify factors associated with pulmonary

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Primary pulmonary vein stenosis

D. Byron Holt, James H. Moller, Sarah Larson, Marck C. Johnson Washington University.United States American Journal of CardiologyAm J Cardiol 2007; 99: 568-572DOI: 10.1016/j.amjcard.2006.09.100 AbstractPrimary pulmonary vein stenosis (PVS) is a rare entity with a high mortality rate. Relatively little is known regarding predictors of outcome or the appropriate timing of intervention. The Pediatric Cardiac Care

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Pulmonary vein stenosis following repair of total anomalous pulmonary venous connection

Eric J. Devaney, Richard G. Ohye, Edward L. Bove University of Michigan.United States Seminars in Thoracic and Cardiovascular Surgery Pediatric Cardiac Surgery AnnualSemin Thorac Cardiovasc Surg Pediatr Card Surg Annu 2006; 51-55.DOI: 10.1053/j.pcsu.2006.02.023 AbstractPulmonary vein stenosis may occur following the repair of total anomalous pulmonary venous connection and carries a poor prognosis. Conventional surgical therapies have

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