Right Heart Failure Associated with Stenosis or Atresia of Pulmonary Veins

Mortality Patterns in Pediatric Pulmonary Vein Stenosis: Insights Into Right Ventricular Systolic Pressure Associations

Daiji Takajo, Paul J. Critser, Michelle Cash, Melissa Magness, Russel Hirsch Cincinnati Children’s Hospital Medical Center and University of Cincinnati.United States Journal of the American Heart AssociationJ Am Heart Assoc 2025;DOI: 10.1161/JAHA.124.037908 AbstractBackground: Pulmonary vein stenosis in children is associated with a poor prognosis. However, the cause and risk factors for mortality remain uncertain.Methods: This retrospective, single-center study […]

Mortality Patterns in Pediatric Pulmonary Vein Stenosis: Insights Into Right Ventricular Systolic Pressure Associations Read More »

Lung transplantation for congenital pulmonary vein stenosis

Eric N. Mendeloff, Thomas L. Spray, Charles B. Huddleston, Nancy D. Bridges, Charles B. Canter, George B. Mallory, Jr. Washington University School of Medicine.United States Annals of Thoracic SurgeryAnn Thorac Surg 1995; 60: 903-906DOI: 10.1016/0003-4975(95)00543-t AbstractBackground: Congenital pulmonary vein stenosis is a uniformly fatal disease when left untreated. Transcatheter techniques (for example, balloon dilation and stent placement)

Lung transplantation for congenital pulmonary vein stenosis Read More »

De Novo and Progressive Pulmonary Vein Stenosis Following Pediatric Heart Transplantation: A Multicenter Retrospective Study

Arene Butto, Conor O’Halloran, James Kuo, Anna Joong, Amanda L. Hauck, Alan Nugent, William Mahle, Paul Tannous Children’s Healthcare of Atlanta. Lurie Children’s Hospital.United States Pediatric TransplantationPediatr Transplant 2024; 28:DOI: 10.1111/petr.14828 AbstractBackground: Pulmonary vein stenosis (PVS) is a rare condition in which neointimal proliferation leads to venous and arterial hypertension. Little is known about PVS after heart

De Novo and Progressive Pulmonary Vein Stenosis Following Pediatric Heart Transplantation: A Multicenter Retrospective Study Read More »

Rare cause of cardiac failure in an infant

Claudio Henriques, Helena Andrade, Antonio Pires Paediatric Hospital.Portugal Cardiology in the YoungCardiol Young 2019; 29: 711-713DOI: 10.1017/S1047951119000428 AbstractCongenital stenosis of the pulmonary veins is a rare condition whose outcome is guarded despite the available treatment options. We report a case of a 6-month-old infant with significant stenosis of all four pulmonary veins. CategoryStenosis or Obstruction of

Rare cause of cardiac failure in an infant Read More »

The impact of right ventricular pressure and function on survival in patients with pulmonary vein stenosis

Michelle C. Sykes, Christina Ireland, Julia E. McSweeney, Emily Rosenholm, Kristofer G. Andren, Thomas J. Kulik Boston Children’s Hospital.United States Pulmonary CirculationPulm Circ 2018;DOI: 10.1177/2045894018776894 AbstractPulmonary vein stenosis (PVS) is associated with pulmonary hypertension (PH), but there is little information regarding the impact of PH on right ventricular (RV) systolic function and survival. We conducted a

The impact of right ventricular pressure and function on survival in patients with pulmonary vein stenosis Read More »

Predictors of Serious Adverse Events and High-Level Cardiorespiratory Support in Patients Undergoing Transcatheter Pulmonary Vein Interventions

Jessica A. Barreto, Kimberlee Gauvreau, Diego Porras, Jesse J. Esch, Nicola Maschietto, Brian Quinn, Lisa Bergersen, Mary Stein, Ryan Callahan Harvard Medical School and Boston Children’s Hospital. University of Pennsylvania Perelman School of Medicine and Children’s Hospital of Philadelphia.United States Pediatric CardiologyPediatr Cardiol 2023;DOI: 10.1007/s00246-023-03129-6 AbstractPatients with pulmonary vein stenosis (PVS) often require frequent transcatheter pulmonary

Predictors of Serious Adverse Events and High-Level Cardiorespiratory Support in Patients Undergoing Transcatheter Pulmonary Vein Interventions Read More »

Abnormalities in embryological development in total anomalous pulmonary venous connection. A case report

Mihaela Balgradean, Eliza Cinteza, C. Cirstoveanu, Augustina Enculescu, Doina Plesca “Marie Skĺodowska-Curie” Emergency Children’s Hospital.Romania Romanian Journal of Morphology and EmbryologyRom J Morphol Embryol 2013; 54: 635-637DOI: Not Available AbstractPulmonary venous system development starts early in embryonic life. Abnormalities in the development of pulmonary venous system occur either by the absence of common pulmonary vein

Abnormalities in embryological development in total anomalous pulmonary venous connection. A case report Read More »

Congenital pulmonary sling, aorto-pulmonary window and pulmonary vein obstruction as a diagnostic and therapeutic challenge in an infant with VACTERL association

Eckardt Trowitzsch, Martin Schneider, Andreas Urban, Boulos Asfour Vestische Kinder- und Jugendklinik, University of Witten/Herdecke.Germany Clinical Research in CardiologyClin Res Cardiol 2006; 95: 338-343DOI: 10.1007/s00392-006-0383-x AbstractIn a newborn with anal atresia and urethral valves an incomplete VACTERL association, was diagnosed and a colon anus praeter was placed. Sweating and heart murmur led to cardiac diagnostics. By

Congenital pulmonary sling, aorto-pulmonary window and pulmonary vein obstruction as a diagnostic and therapeutic challenge in an infant with VACTERL association Read More »

Pulmonary venous stenosis in a premature infant with bronchopulmonary dysplasia: clinical and autopsy findings of these newly associated entities

Steven Christopher Smith, Raja Rabah University of Michigan Health System.United States Pediatric and Developmental PathologyPediatr Dev Pathol 2012; 15: 160-164DOI: 10.2350/11-09-1099-CR.1 AbstractPulmonary venous stenosis is rare and is most commonly found in association with cardiac malformations. Recent studies have associated pulmonary venous stenosis with prematurity, especially with bronchopulmonary dysplasia, although no such case has been documented

Pulmonary venous stenosis in a premature infant with bronchopulmonary dysplasia: clinical and autopsy findings of these newly associated entities Read More »

Significance of the Pulmonary Vascular Bed in Congenital Heart Disease: V. Lesions of the Left Side of the Heart Causing Obstruction of the Pulmonary Venous Return

Charlotte Ferencz, J. Francis Dammann Johns Hopkins University and Hospital. University of Virginia.United States CirculationCirculation 1957; 16:1046-1056DOI: 10.1161/01.cir.16.6.1046 AbstractA microscopic study was made of the lungs of 18 patients with congenital malformations of the heart in which there was obstruction of pulmonary venous drainage. Alterations in various components of the pulmonary vascular bed and of the

Significance of the Pulmonary Vascular Bed in Congenital Heart Disease: V. Lesions of the Left Side of the Heart Causing Obstruction of the Pulmonary Venous Return Read More »