Stenosis or Obstruction of Normal Pulmonary Venous Connections

Long-term outcomes of individualised repair in patients with primary pulmonary vein stenosis

Zhangwei Wang, Yang Yang Beijing Children’s Hospital, National Children’s Medical Center and Capital Medical University.China Cardiology in the YoungCardiol Young 2025; DOI: 10.1017/S1047951124026180 AbstractObjectives: Primary pulmonary vein stenosis is a rare congenital heart condition and carries a poor prognosis. Various surgical techniques have been introduced to treat primary pulmonary vein stenosis. However, there is no consensus on […]

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A New Variant in the GATA6 Gene Associated with Tracheoesophageal Fistula, Pulmonary Vein Stenosis, and Neonatal Diabetes

Flaminia Pugnaloni, Ludovica Martini, Domenico Umberto De Rose, Francesca Landolfo, Paola Giliberti, Rosario Ruta, Antonio Novelli, Novella Rapini, Fabrizio Barbetti, Alessandra Toscano, Andrea Conforti, Pietro Bagolan, Irma Capolupo, Andrea Dotta “Bambino Gesù” Children’s Hospital Istituto di Ricovero e Cura a Carattere Scientifico. University of Rome “Tor Vergata”. Italy Hormone Research in PaediatricsHorm Res Paediatr 2025;

A New Variant in the GATA6 Gene Associated with Tracheoesophageal Fistula, Pulmonary Vein Stenosis, and Neonatal Diabetes Read More »

Combination Chemotherapy in Severe Pulmonary Vein Stenosis-A Case Series

Gabriel Krivenko, Karen Iacono, David Nykanen, Robyn Keen, Robert Sutphin, Michael Farias University of Central Florida. Orlando Health Arnold Palmer Hospital for Children. Boston Children’s Hospital.United States ChildrenChildren 2023; 10: DOI: 10.3390/children10020364 AbstractPulmonary vein stenosis results from a proliferative process that leads to the progressive obstruction of venous return to the left atrium. It is often

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Early Experience With Reverse Double Switch Operation for the Borderline Left Heart

Brandi Braud Scully, Eric N. Feins, Wayne Tworetzky, Sunil Ghelani, Rebecca Beroukhim, Pedro J. Del Nido, Sitaram M. Emani Boston Children’s Hospital and Harvard Medical School.United States Seminars in Thoracic and Cardiovascular SurgerySemin Thorac Cardiovasc Surg 2024; 36: 67-79DOI: 10.1053/j.semtcvs.2022.09.009 AbstractThis study reviews our early experience with the “reverse” double switch operation (R-DSO) for borderline left

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Tricuspid Valve Blood Cysts Mimicking Thrombus or Vegetation on Echocardiogram in a Neonate

Takato Yamasaki, Rebecca Beroukhim, Stephen Sanders, Chrystalle Katte Carreon Boston Children’s Hospital and Harvard Medical School. Mie University Graduate School of Medicine. United States and Japan Pediatric CardiologyPediatr Cardiol 2023; 44: 245-248DOI: 10.1007/s00246-022-02978-x AbstractA 2-month-old male infant, born premature with a birth weight of 865 g, was found to have a tricuspid valve mass mimicking thrombus

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Case report: Rescue treatment with add-on selexipag in a preterm infant with suprasystemic pulmonary hypertension, pulmonary capillary hemangiomatosis, and isolated pulmonary vein stenosis

Hosan Hasan, Klea Hysko, Thomas Jack, Jens Dingemann, Martin Wetzke, Georg Hansmann Hannover Medical School. European Pediatric Pulmonary Vascular Disease Network.Germany Frontiers in Cardiovascular MedicineFront Cardiovasc Med 2022; 9: DOI: 10.3389/fcvm.2022.984698 AbstractAn extremely dystrophic, premature female infant, born at 25 3/7 weeks of gestational age (birth weight: 430 g) with severe pulmonary hypertension (PH), was admitted

Case report: Rescue treatment with add-on selexipag in a preterm infant with suprasystemic pulmonary hypertension, pulmonary capillary hemangiomatosis, and isolated pulmonary vein stenosis Read More »

Transconduit approach for pulmonary vein stenting in an extracardiac Fontan and plastic bronchitis case

Kumiyo Matsuo, Masaki Hirose, Hisaaki Aoki, Futoshi Kayatani Osaka Women’s and Children’s Hospital.Japan British Medical Journals Case ReportsBMJ Case Rep 2022; 13: DOI: 10.1136/bcr-2022-250565 AbstractPlastic bronchitis (PB) is a rare but severe complication in patients following the Fontan operation, the final palliative procedure for single ventricle heart disease. PB is characterised by the formation of rubbery

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Neonatal sutureless pericardial marsupialization for isolated iatrogenic pulmonary vein stenosis

Tomoyuki Iwase, Rajnish K. Garg, Mahmoud A. Al Soufi, Roberto M. Di Donato Al Jalila Children’s Hospital. United Arab Emirates Journal of Cardiac SurgeryJ Card Surg 2022; 37: 3932-3934DOI: 10.1111/jocs.16861 AbstractA 12-day-old girl underwent extended end-to-end aortic arch reconstruction with proximal pulmonary autograft patch augmentation on moderately hypothermic cardiopulmonary bypass. At the end of the procedure,

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Retrograde Pulmonary Vein Recanalization Using Transcatheter Electrosurgery

Saleem I. Almasarweh, James A. Kuo, Holly D. Bauser-Heaton, Vasilis C. Babaliaros, Dennis W. Kim Children’s Healthcare of Atlanta and Emory University Hospital.united States Journal of the American College of Cardiology Case ReportsJACC Case Rep 2022; 4: 592-595DOI: 10.1016/j.jaccas.2022.03.026 AbstractTranscatheter electrosurgery is a wire-based technique used to traverse or cut tissue within blood-filled spaces using alternating

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Pulmonary Vein Stenosis Associated with Germline PIK3CA Mutation

Delphine Yung, Kaitlyn Freeman, Ghayda Mirzaa University of Washington School of Medicine and Seattle Children’s Research Institute. Brotman Baty Institute for Precision Medicine.United States ChildrenChildren 2022; 9: DOI: 10.3390/children9050671 AbstractPulmonary vein stenosis is a rare and frequently lethal childhood disease. There are few known genetic associations, and the pathophysiology is not well known. Current treatments include

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