Stenosis or Obstruction of Pulmonary Veins Following Surgical Repair of Anomalous Pulmonary Venous Connections

Mid-term results of the Lugones procedure for scimitar syndrome repair

Ignacio Lugones, Antonio Gonzalez Calle, Ramón Pérez-Caballero, Giuseppe Pelella, Virginie Fouilloux, Inés A. Martínez, Veronica Laudani, Ashish Katewa, Héctor S. Díliz-Nava, Javier H. López Terrazas, Alexis J. Palacios Macedo-Quenot, Juan Miguel Gil-Jaurena, Daniel A. Klinger, Benjamin Chiostri, Andrés Rosso, Norberto Berber, María Sol De Los Santos, Natalia Troncoso, Victoria E. Zerpa Pacheco, Fernanda Biancolini, Julio

Mid-term results of the Lugones procedure for scimitar syndrome repair Read More »

Imatinib Mesylate and Sirolimus Inhibit Vascular Fibroproliferative Remodeling in Pulmonary Vein Stenosis

Julia Gaal, Sophie C. Doettl, Kerstin Saraci, Cindy Zajac, Alexa von Mueffling, Peter E. Hammer, Magnus von Piechowski, Verena Gebert, Andrei-Antonio M. Caracioni, Daniel Diaz-Gil, Viktoria Weixler, Pedro J. Del Nido, Kathy Jenkins, Ingeborg Friehs Boston Children’s Hospital and Harvard Medical School. German Heart Center of Charité-Universitätsmedizin Berlin.United States and Germany ChildrenChildren 2026; 13:DOI: 10.3390/children13091280

Imatinib Mesylate and Sirolimus Inhibit Vascular Fibroproliferative Remodeling in Pulmonary Vein Stenosis Read More »

A Computational Framework for Quantifying Hemodynamic Burden in Pediatric Pulmonary Vein Stenosis

Manish Bansal, Dan Lior, Avishek Mukherjee, Jeffrey S. Heinle, Athar M. Qureshi, Charles Puelz, Ravi K. Birla Texas Children’s Hospital and Baylor College of Medicine. University of Houston.United States Journal of Thoracic and Cardiovascular SurgeryJ Thorac Cardiovasc Surg 2026;DOI: 10.1016/j.jtcvs.2026.09.007 AbstractBackground: Pulmonary vein stenosis (PVS) is a rare but devastating pediatric disorder characterized by progressive

A Computational Framework for Quantifying Hemodynamic Burden in Pediatric Pulmonary Vein Stenosis Read More »

Combined conventional-to-sutureless repair of the supracardiac total anomalous pulmonary venous drainage

Yaroslav Ivanov, Yaroslav Mykychak. Kira Kuschnerus, Sulejman Abdusalamov, Mi-Young Cho, Joachim Photiadis Deutsches Herzzentrum der Charité.Germany Multimedia Manual of Cardio-Thoracic SurgeryMultimed Man Cardiothorac Surg 2026; DOI: 10.1510/mmcts.2026.071 AbstractThis case describes a combined conventional-to-sutureless repair of the supracardiac form of total anomalous pulmonary venous drainage in a neonate. The diagnosis was established via echocardiography in a

Combined conventional-to-sutureless repair of the supracardiac total anomalous pulmonary venous drainage Read More »

Right Ventricular Function Improves With Pulmonary Vasodilator Treatment in Pediatric Patients With Pulmonary Hypertension and Multivessel Pulmonary Vein Stenosis in a Single Center Cohort

Catherine M. Avitabile, Kimberly Butler, Antara Mondal, David B. Frank, Yan Wang, Devon Ash, Laura Mercer‐Rosa, Michael L. O’Byrne, Ryan Callahan University of Pennsylvania, Perelman School of Medicine and Children’s Hospital of Philadelphia.United States Pulmonary CirculationPulm Circ 2026; 16:DOI: 10.1002/pul2.70346 AbstractPulmonary hypertension (PH) and right ventricular (RV) dysfunction increase mortality in multivessel pediatric pulmonary vein stenosis

Right Ventricular Function Improves With Pulmonary Vasodilator Treatment in Pediatric Patients With Pulmonary Hypertension and Multivessel Pulmonary Vein Stenosis in a Single Center Cohort Read More »

Pulmonary Venous Decompressing Collaterals: Angiographic Characteristics and Impact on Outcomes in Pediatric Pulmonary Vein Stenosis

Ashish Saini, Hui Huang, Andrew Jergel, Rosemary Gray, Dennis W. Kim, James Kuo Children’s Healthcare of Atlanta and Emory University School of Medicine.United States Pediatric CardiologyPediatr Cardiol 2026;DOI: 10.1007/s00246-026-04350-9 AbstractPediatric pulmonary vein stenosis (PVS) is a rare, progressive condition associated with significant morbidity and mortality. While pulmonary venous decompressing collaterals (PVDC) have been described, their clinical

Pulmonary Venous Decompressing Collaterals: Angiographic Characteristics and Impact on Outcomes in Pediatric Pulmonary Vein Stenosis Read More »

Extracorporeal Membrane Oxygenation in Pediatric Pulmonary Hypertension: A Single-Center Cohort to Inform Decision-Making

Taylor M. Smith, Kathryn Restaino, Stuart Lipsitz, Jai Krishan Khurana, Mary P. Mullin, John N. Kheir, Katie M. Moynihan Boston Children’s Hospital, Brigham and Women’s Hospital and Harvard Medical School.United States American Society of Artificial Internal Organs JournalASAIO J 2026;DOI: 10.1097/MAT.0000000000002766 AbstractLimited data describe children with pulmonary hypertension (PH) supported on extracorporeal membrane oxygenation (ECMO). This

Extracorporeal Membrane Oxygenation in Pediatric Pulmonary Hypertension: A Single-Center Cohort to Inform Decision-Making Read More »

Recurrent pulmonary vein stenosis potentially aggravated by posterior compression in a patient with asplenia

Takako Nishino, Makoto Ando Kanazawa Medical University.Japan Journal of Cardiothoracic SurgeryJ Cardiothorac Surg 2026; DOI: 10.1186/s13019-026-04424-y AbstractPulmonary vein stenosis after repair of total anomalous pulmonary venous connection (TAPVC) is a life-threatening complication that frequently recurs, particularly in patients with asplenia. Although intrinsic mechanisms such as ostial narrowing and progressive neointimal proliferation are well recognized, extrinsic mechanical

Recurrent pulmonary vein stenosis potentially aggravated by posterior compression in a patient with asplenia Read More »

Case Report: Post-Total anomalous pulmonary venous connection pulmonary hypertension – novel treatment using sirolimus and atrial flow regulator implantation

Stasa Krasic, Antony Hermuzi, Ivan Dizdarevic, Vesna Topic, Nevena Djorovic, Mihail Basa, Vladislav Vukomanovic Mother and Child Health Institute of Serbia and University of Belgrade. Freeman Hospital and Newcastle upon Tyne Hospitals NHS Foundation Trust.Serbia and United Kingdom Frontiers in Cardiovascular MedicineFront Cardiovasc Med 2026; 13:DOI: 10.3389/fcvm.2026.1783773 AbstractObjective: In patients who have undergone surgical repair of TAPVC

Case Report: Post-Total anomalous pulmonary venous connection pulmonary hypertension – novel treatment using sirolimus and atrial flow regulator implantation Read More »

Therapeutic Targets for Pediatric Pulmonary Vein Stenosis: Insights from Animal Models

Siqi She, Debao Li, Qi Sun, Lincai Ye Shanghai Children’s Medical Center and Shanghai Jiao Tong University School of Medicine. Children’s Hospital of Fudan University and National Children’s Medical Center.China ChildrenChildren 2026; 13:DOI: 10.3390/children13050677 AbstractPulmonary vein stenosis (PVS) is a rare and devastating condition affecting infants and children, characterized by progressive intimal hyperplasia, myofibroblast proliferation, and

Therapeutic Targets for Pediatric Pulmonary Vein Stenosis: Insights from Animal Models Read More »