Stenosis or Obstruction of Pulmonary Veins Following Surgical Repair of Anomalous Pulmonary Venous Connections

Right Ventricular Function Improves With Pulmonary Vasodilator Treatment in Pediatric Patients With Pulmonary Hypertension and Multivessel Pulmonary Vein Stenosis in a Single Center Cohort

Catherine M. Avitabile, Kimberly Butler, Antara Mondal, David B. Frank, Yan Wang, Devon Ash, Laura Mercer‐Rosa, Michael L. O’Byrne, Ryan Callahan University of Pennsylvania, Perelman School of Medicine and Children’s Hospital of Philadelphia.United States Pulmonary CirculationPulm Circ 2026; 16:DOI: 10.1002/pul2.70346 AbstractPulmonary hypertension (PH) and right ventricular (RV) dysfunction increase mortality in multivessel pediatric pulmonary vein stenosis […]

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Pulmonary Venous Decompressing Collaterals: Angiographic Characteristics and Impact on Outcomes in Pediatric Pulmonary Vein Stenosis

Ashish Saini, Hui Huang, Andrew Jergel, Rosemary Gray, Dennis W. Kim, James Kuo Children’s Healthcare of Atlanta and Emory University School of Medicine.United States Pediatric CardiologyPediatr Cardiol 2026;DOI: 10.1007/s00246-026-04350-9 AbstractPediatric pulmonary vein stenosis (PVS) is a rare, progressive condition associated with significant morbidity and mortality. While pulmonary venous decompressing collaterals (PVDC) have been described, their clinical

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Extracorporeal Membrane Oxygenation in Pediatric Pulmonary Hypertension: A Single-Center Cohort to Inform Decision-Making

Taylor M. Smith, Kathryn Restaino, Stuart Lipsitz, Jai Krishan Khurana, Mary P. Mullin, John N. Kheir, Katie M. Moynihan Boston Children’s Hospital, Brigham and Women’s Hospital and Harvard Medical School.United States American Society of Artificial Internal Organs JournalASAIO J 2026;DOI: 10.1097/MAT.0000000000002766 AbstractLimited data describe children with pulmonary hypertension (PH) supported on extracorporeal membrane oxygenation (ECMO). This

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Recurrent pulmonary vein stenosis potentially aggravated by posterior compression in a patient with asplenia

Takako Nishino, Makoto Ando Kanazawa Medical University.Japan Journal of Cardiothoracic SurgeryJ Cardiothorac Surg 2026; DOI: 10.1186/s13019-026-04424-y AbstractPulmonary vein stenosis after repair of total anomalous pulmonary venous connection (TAPVC) is a life-threatening complication that frequently recurs, particularly in patients with asplenia. Although intrinsic mechanisms such as ostial narrowing and progressive neointimal proliferation are well recognized, extrinsic mechanical

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Case Report: Post-Total anomalous pulmonary venous connection pulmonary hypertension – novel treatment using sirolimus and atrial flow regulator implantation

Stasa Krasic, Antony Hermuzi, Ivan Dizdarevic, Vesna Topic, Nevena Djorovic, Mihail Basa, Vladislav Vukomanovic Mother and Child Health Institute of Serbia and University of Belgrade. Freeman Hospital and Newcastle upon Tyne Hospitals NHS Foundation Trust.Serbia and United Kingdom Frontiers in Cardiovascular MedicineFront Cardiovasc Med 2026; 13:DOI: 10.3389/fcvm.2026.1783773 AbstractObjective: In patients who have undergone surgical repair of TAPVC

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Therapeutic Targets for Pediatric Pulmonary Vein Stenosis: Insights from Animal Models

Siqi She, Debao Li, Qi Sun, Lincai Ye Shanghai Children’s Medical Center and Shanghai Jiao Tong University School of Medicine. Children’s Hospital of Fudan University and National Children’s Medical Center.China ChildrenChildren 2026; 13:DOI: 10.3390/children13050677 AbstractPulmonary vein stenosis (PVS) is a rare and devastating condition affecting infants and children, characterized by progressive intimal hyperplasia, myofibroblast proliferation, and

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Pathogenesis, Evaluation, and Management of Pulmonary Vein Stenosis: JACC Review Topic of the Week

Trevor Simard, Dhruv Sarma, William R. Miranda, Charles Jain, Jason H. Anderson, Jeremy D. Collins, Abdallah El Sabbagh, Aravdeep Jhand, Tobias Peikert, Guy S. Reeder, Thomas M. Munger, Douglas L. Packer, David R. Holmes Mayo Clinic.United States Journal of the American College of CardiologyJ Am Coll Cardiol 2023; 81: 2361-2373DOI: 10.1016/j.jacc.2023.04.016 AbstractPulmonary vein stenosis (PVS) can

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Surgical and Catheter-Based Intervention in Pediatric Pulmonary Vein Stenosis

Daiji Takajo, Paul J. Critser, Awais Ashfaq, Russel Hirsch Cincinnati Children’s Hospital Medical Center and University of Cincinnati. University of Texas Southwestern Medical Center. United States Pediatric CardiologyPediatr Cardiol 2026; DOI: 10.1007/s00246-026-04266-4 AbstractBackground: Pulmonary vein stenosis (PVS) is a rare but serious condition in children, often requiring surgical or catheter-based interventions. The initial optimal treatment strategy remains

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Pediatric Pulmonary Vein Stenosis and Treatment

Joice Prodigios, Stephanie El Omeiri, Marcus Meneses, Bethelhem Belachew, Hansel J. Otero, David M. Biko, Jordan B. Rapp Children’s Hospital of Philadelphia and Perelman School of Medicine at The University of Pennsylvania.United States Seminars in RoentenologySemin Roentenol 2025; DOI: 10.1053/j.ro.2025.09.006 AbstractPulmonary vein stenosis (PVS) is an uncommon but often progressive condition in children, associated with high

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Outcomes and Patency Following Surgical Repair of Previously Stented Pulmonary Veins in Pediatric Patients

Allison Beckham Davila, Mariana Chavez, Kimberlee Gauvreau, Christina Ireland, Kathy J. Jenkins, Michael Farias, Eric N. Feins, Christopher W. Baird Boston Children’s Hospital and Harvard Medical School. Lurie Children’s Hospital of Chicago and Feinberg School of Medicine.United States Annals of Thoracic SurgeryAnn Thorac Surg 2026;DOI: 10.1016/j.athoracsur.2026.03.056 AbstractBackground: The study objective was to evaluate surgical outcomes of patients

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