Symptoms and Quality of Life Associated with Pulmonary Venous Obstruction

Unilateral pulmonary vein atresia: A rare case of hemoptysis

Cindy S. DeMastes-Crabtree, Edward Kim, Ronald L. Morton University of Louisville and Kosair Children’s Hospital. United States Respiratory Medicine Case ReportsRespir Med Case Rep 2015; 15: 83-84DOI: 10.1016/j.rmcr.2015.05.009 AbstractWe present a rare case of hemoptysis secondary to isolated unilateral pulmonary vein atresia. Isolated pulmonary vein atresia is a rare condition in which patients typically acquire a […]

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Improved gas exchange after pneumonectomy in an adult with incomplete pulmonary vein atresia

Tjip S. van der Werf, Gregor P. M. Mannes, Joffre M. Hew, Rene G. Grevink, Thomas W. van der Mark, Tjark Ebels, Gerard H. Koeter Groningen University Hospital.Netherlands Thorax Thorax 1994; 49:723-725DOI: 10.1136/thx.49.7.723 AbstractAtresia of the pulmonary veins of the left lung and the right upper lobe with moderate pulmonary hypertension was diagnosed in a 20

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Isolated unilateral pulmonary vein atresia in adult patients: a case report and literature review

Min Zhang, Qing-Chen Wu, Cheng Zhang, Qiang Li, Ying-Jiu Jiang, Dan Chen First Affiliated Hospital of Chongqing Medical University.China Heart Surgery ForumHeart Surg Forum 2010; 13: E370-E372DOI: 10.1532/HSF98.20101078. https://journal.hsforum.com/index.php/HSF/article/view/55/54 AbstractUnilateral pulmonary vein atresia is a rare abnormality that usually presents in infants with recurrent hemoptysis and pneumonia. Presentation in adulthood without additional congenital heart disease is

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Congenital unilateral pulmonary vein atresia: A rare disease with successful outcome in a child

Raja Sumandatta Aduri, Javid Raja, Ganesh Kumar Munirathinam, Raghuraman Soundararajan, Arun Sharma, Sachin Mahajan 29751Postgraduate Institute of Medical Education and Research.India Asian Cardiovascular and Thoracic AnnalsAsian Cardiovasc Thorac Ann 2022; 30: 943-946DOI: 10.1177/02184923221115972 AbstractUnilateral pulmonary vein atresia is a rare congenital anomaly that may occur in association with other congenital heart diseases. We report a rare

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Isolated unilateral pulmonary vein atresia with hemoptysis in a child: A case report and literature review

Changqing Tang, Hongyu Duan, Kaiyu Zhou, Yimin Hua, Xiaoliang Liu, Yifei Li, Chuan Wang West China Institute of Women and Children’s Health, West China Second University Hospital, Sichuan University West China Medical School of Sichuan University. China MedicineMedicine 2018; DOI: 10.1097/MD.0000000000011882 AbstractRationale: Hemoptysis is an uncommon chief complaint but a distressing symptom in pediatric patients. Due to

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Mediastinal and hilar soft tissue mass-like lesions in congenital unilateral pulmonary vein atresia: A retrospective review of seven pediatric patients

Reiko Okamoto, Osamu Miyazaki, Hidekazu Aoki, Yoshiyuki Tsutsumi, Mikiko Miyasaka, Minako Hoshiai, Shunsuke Nosaka National Center for Child Health and Development. Yamanashi Prefectural Central Hospital.Japan Pediatrics InternationalPediatr Int 2020; 62: 1234-1240DOI: 10.1111/ped.14307 AbstractBackground: Congenital unilateral pulmonary vein atresia (CUPVA) is known to lead to the formation of an abnormal confluent mediastinal and hilar soft tissue mass, thoracic

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Unilateral pulmonary vein atresia: diagnostic dilemma unfolded on imaging

Basavaraj Biradar, Arun Sharma, Amarinder Singh Malhi, Sanjeev Kumar All India Institute of Medical Sciences.India British Medical Journal Case ReportsBMJ Case Rep 2018;DOI: 10.1136/bcr-2017-224154 AbstractUnilateral pulmonary vein atresia is a rare entity, usually congenital in origin. It is thought to result from failure of incorporation of common pulmonary vein to left atrium. Patients often present with

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Unilateral pulmonary vein atresia presenting with recurrent haemoptysis in a child: a case report

Martin Ngie Liong Wong, Ing Ping Tang, Yek Kee Chor, Kiew Siong Lau, Anne Rachel John, King Ching Hii, Olive Pei Yi Lee, Wooi Kok Lim, Hannah Pei Koon Tan Sarawak Heart Center. Universiti Malaysia. Sarawak General Hospital. Miri Hospital.Malaysia BioMedical Central PediatricsBMC Prediatr 2020; 20:DOI: 10.1186/s12887-020-02348-7 AbstractBackground: Haemoptysis is an uncommon presenting symptom in children and

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Imaging findings of an asymptomatic child with pulmonary vein atresia

Taísa Davaus Gasparetto, Pedro Daltro, Edson Marchiori Federal University of Rio de Janeiro.Brazil Pediatric RadiologyPediatr Radiol 2010; 40: 1458-1459DOI: 10.1007/s00247-010-1663-1 AbstractAbstract Not Available CategoryAbsence or Atresia of Normal Pulmonary Venous ConnectionsDiagnostic Testing. NoninvasiveSymptoms and Quality of Life Associated with Pulmonary Venous Obstruction Year of Publication: 2010 Age Focus: Pediatric Article Type: Case Reports or Retrospective Observations in Small Groups

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Unilateral pulmonary vein atresia presenting with recurrent hydrothorax in an adult: A case report

Yan Wang, Shuangshuang Jiang, Jiasheng Yang, Ruilin Sun Guangdong Second Provincial General Hospital.China Respiratory Medicine Case ReportsRespir Med Case Rep 2022; DOI: 10.1016/j.rmcr.2022.101711 AbstractUPVA (Unilateral pulmonary vein atresia) is the failure of connection between the common pulmonary vein and the left atrium. UPVA is a rare malformation of common pulmonary vein caused by embryonic development defects.

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