Complete absence of pulmonary veins

M. A. Ralston, D. W. Teske

Children’s Hospital, Columbus.
United States

Clinical Cardiology
Clin Cardiol 1988; 11: 272-275
DOI: 10.1002/clc.4960110415

Abstract
Various types of pulmonary venous return abnormalities have been described in the literature. This report presents a case in which a 4-h-old neonate presented with cyanotic heart disease and respiratory distress. This neonate was subsequently shown to have complete absence of the pulmonary veins (CAPV), a previously undescribed malformation. The case summary describes the physical findings, radiographic and electrocardiographic features, cardiac catheterization data, and results from autopsy. A discussion of the case, theories of embryological etiology for this malformation, and differential diagnoses follow. Surgical treatment for CAPV is not yet possible.

Category
Absence or Atresia of Normal Pulmonary Venous Connections
Diagnostic Testing. Noninvasive
Diagnostic Testing. Invasive
Pulmonary Venous Pathology

Year of Publication: 1988

Age Focus: Pediatric

Article Type: Case Reports or Retrospective Observations in Small Groups of Patients (≤10 patients)

Article Access: Free PDF File or Full Text Article Available Through PubMed or DOI: Yes