Congenital Heart Surgery Nomenclature and Database Project: pulmonary venous anomalies

J. René Herlong, James J. Jaggers, Ross M. Ungerleider

Duke University Medical Center.
United States

Annals of Thoracic Surgery
Ann Thorac Surg 2000; 69 (4 Suppl): S56-S69
DOI: 10.1016/s0003-4975(99)01237-0

Abstract
The extant nomenclature for pulmonary venous anomalies is reviewed for the purpose of establishing a unified reporting system. The subject was debated and reviewed by members of the STS-Congenital Heart Surgery Database Committee and representatives from the European Association for Cardiothoracic Surgery. All efforts were made to include all relevant nomenclature categories using synonyms where appropriate. The basis for classification are the prenatal errors of embryologic development. The major categories include: partially anomalous pulmonary venous connection, totally anomalous pulmonary venous connection, atresia of the common pulmonary vein, cor triatriatum, and stenosis or abnormal number of pulmonary veins. A comprehensive database set is presented that is based on a hierarchical scheme. Data are entered at various levels of complexity and detail that can be determined by the clinician. These data can lay the foundation for comprehensive risk stratification analyses. A minimum database set is also presented that will allow for data sharing and would lend itself to basic interpretation of trends. Potential diagnostic-related risk factors are presented.

Category
Stenosis or Obstruction of Normal Pulmonary Venous Connections

Year of Publication: 2000

Age Focus: Pediatric

Article Type: Review

Article Access: Free PDF File or Full Text Article Available Through PubMed or DOI: No