Congenital unilateral pulmonary vein atresia: radiologic findings in three adult patients

Laura E. Heyneman, Robert L. Nolan, J. Kevin Harrison, H. Page McAdams

Duke University Medical Center.
United States

American Journal of Roentgenology
AJR Am J Roentgenol 2001; 177: 681-685
DOI: 10.2214/ajr.177.3.1770681

Abstract
Objective: The purpose of our study is to describe the radiologic findings of adult patients presenting with congenital unilateral pulmonary vein atresia.
Conclusion: Chest radiography in affected patients typically reveals a small hemithorax and ipsilateral pulmonary artery as well as ipsilateral septal thickening. CT shows, in addition, ground-glass attenuation, the absence of a pulmonary vein connection to the left atrium, and abundant mediastinal venous collateral vessels. MR imaging is helpful in further characterizing the vascular abnormalities. Angiography may help to confirm the diagnosis.

Category
Absence or Atresia of Normal Pulmonary Venous Connections
Length of Life Associated with Pulmonary Venous Obstruction
Symptoms and Quality of Life Associated with Pulmonary Venous Obstruction
Diagnostic Testing. Noninvasive
Diagnostic Testing. Invasive

Year of Publication: 2001

Age Focus: Adult

Article Type: Case Reports or Retrospective Observations in Small Groups of Patients (≤10 patients)

Article Access: Free PDF File or Full Text Article Available Through PubMed or DOI: Yes