Stephanie M. Tsoi, Roberta L. Keller, Loren D. Sacks, Vinod Sebastian, Sanjeev A. Datar, Michael A. Smith, Jason Boehme, Jeffrey R. Fineman, Elena K. Amin
University of California San Francisco.
United States
Pediatric Cardiology
Pediatr Cardiol 2026;
DOI: 10.1007/s00246-026-04434-6
Abstract
Pediatric pulmonary vein stenosis (PVS) is associated with high morbidity and mortality. We describe a case series of pediatric patients with advanced multivessel PVS who underwent cardiac catheterization with veno-arterial extracorporeal life support (VA-ECLS) to prevent cardiac arrest around high-risk pulmonary vein angioplasty and/or stent placement. VA-ECLS provided hemodynamic and respiratory stabilization, allowing completion of technically complex interventions in critically-ill pediatric patients who may not have otherwise tolerated catheterization. Using VA-ECLS in this setting requires a thorough assessment of risks versus benefits and specific patient criteria for consideration. This series highlights the potential role of VA-ECLS as an adjunctive strategy during high-risk catheter-based interventions for pediatric PVS to improve quality of life and lengthen lifespan.
Category
Stenosis or Obstruction of Normal Pulmonary Venous Connections
Pulmonary Hypertension Associated with Stenosis or Atresia of Pulmonary Veins
Right Heart Failure Associated with Stenosis or Atresia of Pulmonary Veins
Catheter-mediated Interventions: Efficacy or Lack of Efficacy
Catheter-mediated Interventions: Adverse Effects or Lack of Adverse Effects
Year of Publication: 2026
Age Focus: Pediatric
Article Type: Case Reports or Retrospective Observations in Small Groups of Patients (≤10 patients)
Article Access: Free PDF File or Full Text Article Available Through PubMed or DOI: Yes