Hemoptysis from bronchial varices associated with pulmonary vein stenosis: role of surgical repair

A. Walsh, G. Canny, C.J. McMahon, J. M. Redmond, P. McNally

Our Lady’s Children’s Hospital.
Ireland

Pediatric Pulmonology
Pediatr Pulmonol 2013; 48: 838-840
DOI: 10.1002/ppul.22659

Abstract
We present the case of a 6-year-old child who presented with an episode of life threatening hemoptysis. Investigations revealed multiple areas of endobronchial varices and abnormal pleural vessels as well as severe left pulmonary vein stenosis and an atrial septal defect (ASD). After extensive work up and consultation he underwent repair of the left pulmonary vein using a sutureless technique and ASD closure. This resulted in a marked improvement in the appearances of the left lung. The bronchial varices in the right lung remain unchanged. No further hemoptysis has occurred and the child continues to be monitored.

Category
Stenosis or Obstruction of Normal Pulmonary Venous Connections
Symptoms and Quality of Life Associated with Pulmonary Venous Obstruction
Surgical Interventions for Pulmonary Venous Obstruction After the Onset of Disease

Year of Publication: 2013

Age Focus: Pediatric

Article Type: Case Reports or Retrospective Observations in Small Groups of Patients (≤10 patients)

Article Access: Free PDF File or Full Text Article Available Through PubMed or DOI: No