Hypoplastic right lung associated with right pulmonary vein stenosis and systemic collateral

Anant Khositseth, Suvipaporn Siriporpitak, Preecha Laohakunakorn

Ramathibodi Hospital Mahidol University.
Thailand

Congenital Heart Disease
Congenit Heart Dis 2010; 5: 76-80
DOI: 10.1111/j.1747-0803.2009.00324.x

Abstract
We present a case of a 6-month-old girl diagnosed as unilateral pulmonary vein stenosis (right inferior pulmonary vein) with dextroposition of the heart, hypoplastic right lung, hypoplastic right pulmonary artery, collateral from the descending aorta supplied right lower lung, connection between collateral and right pulmonary artery with retrograde flow from right pulmonary artery into main pulmonary artery, and right superior and middle pulmonary vein agenesis. A combined modality of imaging including chest film, echocardiography, multidetector computerized tomography, and the cardiac catheterization nicely demonstrated all of the unique and rare congenital abnormalities.

Category
Stenosis or Obstruction of Normal Pulmonary Venous Connections
Diagnostic Testing. Noninvasive
Diagnostic Testing. Invasive

Year of Publication: 2010

Age Focus: Pediatric

Article Type: Case Reports or Retrospective Observations in Small Groups of Patients (≤10 patients)

Article Access: Free PDF File or Full Text Article Available Through PubMed or DOI: No