Isolated unilateral pulmonary vein atresia in adult patients: a case report and literature review

Min Zhang, Qing-Chen Wu, Cheng Zhang, Qiang Li, Ying-Jiu Jiang, Dan Chen

First Affiliated Hospital of Chongqing Medical University.
China

Heart Surgery Forum
Heart Surg Forum 2010; 13: E370-E372
DOI: 10.1532/HSF98.20101078. https://journal.hsforum.com/index.php/HSF/article/view/55/54

Abstract
Unilateral pulmonary vein atresia is a rare abnormality that usually presents in infants with recurrent hemoptysis and pneumonia. Presentation in adulthood without additional congenital heart disease is rare but does occur. Anatomic variations in the pulmonary vessels that supply and drain the affected lung can explain the mildly symptomatic process. The diagnosis of isolated unilateral pulmonary vein atresia is usually made angiographically. Pneumonectomy is indicated once symptoms or complications are present so that irreversible pulmonary hypertension can be avoided.

Category
Absence or Atresia of Normal Pulmonary Venous Connections
Symptoms and Quality of Life Associated with Pulmonary Venous Obstruction

Year of Publication: 2010

Age Focus: Adult

Article Type: Case Reports or Retrospective Observations in Small Groups of Patients (≤10 patients). Literature Review and Analysis.

Article Access: Free PDF File or Full Text Article Available Through PubMed or DOI: Yes, through the Heart Surgery Forum link