Phillip S. Naimo, Yves d’Udekem, Christian P. Brizard, Igor E. Konstantinov
Royal Children’s Hospital and University of Melbourne. Murdoch Children’s Research Institute.
Australia
Interactive CardioVascular and Thoracic Surgery
Interact Cardiovasc Thorac Surg 2015; 21: 254–256
DOI: 10.1093/icvts/ivv133
Abstract
Herein, we report a case series of patients who underwent repair of left partial anomalous pulmonary venous connection (L-PAPVC) via anastomosing the anomalous pulmonary vein (PV) to the left atrial appendage. Fifteen children underwent repair of L-PAPVC between 1980 and 2014. The median age at surgery was 3.6 years (range: 5 days to 17.2 years). Concomitant anomalies were present in 87% (13/15). There were no early deaths. There was 1 late death occurring 63 days following surgical repair due to pneumococcal septicaemia in a patient with prior atrial septal defect closure and Ehlers-Danlos syndrome. The overall survival rate was 93.7% at 15 years. A single patient (1/15, 7%) required reoperation 1 year after L-PAPVC repair for PV stenosis due to several thrombi located throughout the PV. The rate of freedom from PV reoperation was 90% at 10 years. The follow-up was 100% complete with a median time of 11 years (range: 52 days to 20 years). To our knowledge, this is the youngest cohort of patients who have undergone surgical repair of L-PAPVC. Repair of L-PAPVC in children can be achieved via anastomosis of the anomalous vessel to the left atrial (LA) with excellent outcomes. The rate of anastomotic stenosis at the site of implantation on the LA is low.
Category
Stenosis or Obstruction of Pulmonary Veins Following Surgical Repair of Anomalous Pulmonary Venous Connections
Incidence or Prevalence of Disease
Surgical Interventions to Prevent or Limit Disease Associated with Repair of Anomalous Pulmonary Venous Connections or Heart Transplantation
Year of Publication: 2015
Age Focus: Pediatric
Article Type: Retrospective Observational Cohort Studies (>10 patients)
Article Access: Free PDF File or Full Text Article Available Through PubMed or DOI: Yes