Postrepair Pulmonary Vein Stenosis: Addressing Anatomic and Patient Risk Factors to Improve Outcomes

Alessia Di Nardo, Elizabeth D. Persaud, Rachel D. Vanderlaan

University of Toronto and Hospital for Sick Children.
Canada

Seminars in Thoracic and Cardiovascular Surgery Pediatric Cardiac Surgery Annual
Semin Thorac Cardiovasc Surg Pediatr Card Surg Annu 2025; 28: 107-116
DOI: 10.1053/j.pcsu.2025.02.008

Abstract
Surgical results for correction of total anomalous pulmonary venous connection (TAPVC) have improved in the current era. Postrepair pulmonary vein stenosis (PR-PVS) remains a major complication following TAPVC repair, often necessitating multiple reinterventions, and impacting patient outcomes. Considerations for patient and anatomical risk factors, surgical techniques for primary TAPVC repair, as well PR-PVS postoperative surveillance and management will be reviewed. We will also touch on emerging areas of research related to PR-PVS pathogenesis and incorporation of patient-specific simulation for surgical planning in TAPVC.

Category
Stenosis or Obstruction of Pulmonary Veins Following Surgical Repair of Anomalous Pulmonary Venous Connections
Surgical Interventions to Prevent or Limit Disease Associated with Repair of Anomalous Pulmonary Venous Connections or Heart Transplantation

Year of Publication: 2025

Age Focus: Pediatric

Article Type: Review

Article Access: Free PDF File or Full Text Article Available Through PubMed or DOI: No