Pulmonary hypertension secondary to partial pulmonary venous obstruction in a child with Cantu syndrome

Daisuke Kobayashi, Amanda L. Cook, Derek A. Williams

Wake Forest University School of Medicine.
United States

Pediatric Pulmonology
Pediatr Pulmonol 2010; 5: 727-729
DOI: 10.1002/ppul.21215

Abstract
We report on an African-American male with Cantu syndrome who required a pericardial window for a significant pericardial effusion in infancy and was subsequently found to have partial pulmonary venous obstruction (PVO) leading to pulmonary hypertension. Measurement of bilateral pulmonary capillary wedge pressures is important to uncover partial PVO.

Category
Stenosis or Obstruction of Normal Pulmonary Venous Connections
Pulmonary Hypertension Associated with Stenosis or Atresia of Pulmonary Veins
Genetic Factors Influencing the Onset, Severity or Outcome of Disease
Patient Factors Influencing the Onset, Severity or Outcome of Disease
Diagnostic Testing. Invasive

Year of Publication: 2010

Age Focus: Pediatric

Article Type: Case Reports or Retrospective Observations in Small Groups of Patients (≤10 patients)

Article Access: Free PDF File or Full Text Article Available Through PubMed or DOI: No