Daniel I. McLennan, Elyan C. Ruiz Solano, Stephanie S. Handler, Joy Lincoln, Michael E. Mitchell, Edward C. Kirkpatrick
Medical College of Wisconsin.
United States
Frontiers in Pediatrics
Front Pediatr 2021;
DOI: 10.3389/fped.2021.747812
Abstract
Pulmonary Vein Stenosis (PVS) is a rare disease with a prevalence of around 1. 7 cases per 100,000 children under 2 years old. Treatment options for this disease have not provided great results and pathophysiology of this condition is still poorly understood. Here, we will review the history of PVS including diagnostic tools and treatments, the current management approach, and what the future holds for this devastating disease.
Category
Stenosis or Obstruction of Normal Pulmonary Venous Connections
Stenosis or Obstruction of Pulmonary Veins Following Surgical Repair of Anomalous Pulmonary Venous Connections
Incidence or Prevalence of Disease
Diagnostic Testing. Noninvasive
Catheter-mediated Interventions: Efficacy or Lack of Efficacy
Surgical Interventions to Prevent or Limit Disease Associated with Repair of Anomalous Pulmonary Venous Connections or Heart Transplantation
Surgical Interventions for Pulmonary Venous Obstruction After the Onset of Disease
Year of Publication: 2021
Age Focus: Pediatric
Article Type: Review
Article Access: Free PDF File or Full Text Article Available Through PubMed or DOI: Yes