Fany Corvol, Sébastien Hascoet, Emmanuel Le Bret, Nadia Nathan
Sorbonne University. Université Paris-Saclay, Marie-Lannelongue Surgical Centre. Ramsay Santé, Clinique du Sport. Sorbonne University.
France
British Medical Journal Case Reports
BMJ Case Rep 2024; 17:
DOI: 10.1136/bcr-2024-259955
Abstract
Scimitar syndrome is characterised by right lung hypoplasia and abnormal pulmonary venous return, known as the ‘scimitar vein’. We report the case of an infant girl with scimitar syndrome who developed a severe respiratory distress mimicking asthma. Pulmonary hypertension (PH) was diagnosed, attributed to scimitar vein stenosis and a left-to-right shunt. Scimitar vein stenosis, a rare complication of scimitar syndrome, can lead to severe PH, highlighting the importance of prompt management in specialised care centres.
Category
Stenosis or Obstruction of Pulmonary Veins: Other Categories (Stenosia of an Anomalous Pulmonary Vein)
Pulmonary Hypertension Associated with Stenosis or Atresia of Pulmonary Veins
Year of Publication: 2024
Age Focus: Pediatric
Article Type: Case Reports or Retrospective Observations in Small Groups of Patients (≤10 patients)
Article Access: Free PDF File or Full Text Article Available Through PubMed or DOI: No