Yifan Guo, Chengbin He, Jianmin Cheng, Fenglei Dong, Bo Ghen
Second Affiliated Hospital and Yuying Children’s Hospital of Wenzhou Medical University.
China
International Journal of Medical Radiology
Int J Med Radiol 2019; 42: 94-98
DOI10.19300/j.2019.L6057;
Abstract
Objective: To investigate the thoracic imaging features of congenital unilateral pulmonary venous atresia (UPVA).
Methods: Clinical manifestations and imaging features of two patients with UPVA were analyzed retrospectively, and relevant literatures were reviewed.
Results: Chest X-ray and CT scan showed a reduced thorax volume of the affected side with mediastinum shift to the affected side, and diffuse reticular opacities or honeycomb in the ipsilateral lung. Furthermore, a low attenuation soft tissue was seen at the affected side pulmonary hilum and mediastinum, and its lateral margin of lung showed a sharp protuberance along the bronchovascular bundle. CT angiography revealed the affected margin of the left atrium was completely smooth without evidence of rudimentary pulmonary veins, and no anomalous pulmonary venous drainage was formed at other sites.
Conclusions: The clinical manifestations of UPVA are lack of specificity. The chest imaging of UPVA has certain characteristics, and the ‘pendular movement of mediastinum’ is a rare imaging feature of this disease.
Category
Absence or Atresia of Normal Pulmonary Venous Connections
Diagnostic Testing. Noninvasive
Year of Publication: 2019
Age Focus: Pediatric
Article Type: Case Reports or Retrospective Observations in Small Groups of Patients (≤10 patients)
Article Access: Free PDF File or Full Text Article Available Through PubMed or DOI: No (Chinese Language)