Total Anomalous Pulmonary Venous Connection: Preoperative Anatomy, Physiology, Imaging, and Interventional Management of Postoperative Pulmonary Venous Obstruction

Matthew D. Files, Brian Morray

Seattle Children’s Hospital.
United States

Seminars in Cardiothoracic and Vascular Anesthesia
Semin Cardiothorac Vasc Anesth 2017; 21: 123-131
DOI: 10.1177/1089253216672442

Abstract
Total anomalous pulmonary venous connection refers to a spectrum of cardiac anomalies where the pulmonary veins fail to return to the left atrium and the pulmonary venous blood returns through a systemic vein or directly to the right atrium. There is a wide anatomical variety of venous connections and degrees of pulmonary venous obstruction that affect the presentation, surgical repair, and outcomes. In this review, we explore the preoperative physiology, echocardiographic diagnosis, and approach to postoperative complications.

Category
Stenosis or Obstruction of Pulmonary Veins Following Surgical Repair of Anomalous Pulmonary Venous Connections
Diagnostic Testing. Noninvasive
Catheter-mediated Interventions: Efficacy or Lack of Efficacy
Surgical Interventions for Pulmonary Venous Obstruction After the Onset of Disease

Year of Publication: 2017

Age Focus: Pediatric

Article Type: Review

Article Access: Free PDF File or Full Text Article Available Through PubMed or DOI: No