Unilateral absence or extreme hypoplasia of pulmonary veins

H. M. Kingston, R. G. Patel, G. H. Watson

Royal Manchester Children’s Hospital.
United Kingdom

British Heart Journal
Brit Heart J 1983; 49: 148-153
DOI: 10.1136/hrt.49.2.148

Abstract
Three children with recurrent chest symptoms and signs caused by unilateral atresia or absence of the pulmonary veins are described, with a discussion of the seven reported cases of unilateral congenital pulmonary venous obstruction. The condition is rare but should enter into the differential diagnosis of recurrent unilateral pulmonary infection or oedema. Pulmonary arteriography is necessary and pulmonary artery wedge angiography is the most informative diagnostic procedure.

Category
Stenosis or Obstruction of Normal Pulmonary Venous Connections
Absence or Atresia of Normal Pulmonary Venous Connections
Pulmonary Hypertension Associated with Stenosis or Atresia of Pulmonary Veins
Patient Factors Influencing the Onset, Severity or Outcome of Disease
Symptoms and Quality of Life Associated with Pulmonary Venous Obstruction
Length of Life Associated with Pulmonary Venous Obstruction
Diagnostic Testing. Invasive
Pulmonary Venous Pathology

Year of Publication: 1983

Age Focus: Pediatric

Article Type: Case Reports or Retrospective Observations in Small Groups of Patients (≤10 patients). Literature Review and Analysis.

Article Access: Free PDF File or Full Text Article Available Through PubMed or DOI: Yes