Unilateral pulmonary vein atresia: Diagnosis and treatment

Antoine T. Nasrallah, Charles E. Mullins, Don Singer, Gunyon Harrison, Dan G. McNamara

Baylor College of Medicine.
United States

American Journal of Cardiology
Am J Cardiol 1975; 36: 969-973
DOI: 10.1016/0002-9149(75)90092-2

Abstract
The clinical, hemodynamic, angiographic and pathologic features of unilateral pulmonary vein atresia in a 16 month old boy are described. The relevant findings were symptoms and signs of influenza, roentgenographic evidence of unilateral diffuse interstitial edema, prominent interlobar fissures and pleural effusion, absence of abnormal cardiac structure and prominent unilateral bronchial circulation. Angiocardiography was necessary for a definitive diagnosis and revealed the lack of a site of entry for venous blood from the right lung into the circulation. The patient was treated successfully by a right pneumonectomy. The histologic hallmark in this case was extensive intimal fibrosis of the pulmonary veins.

Category
Absence or Atresia of Normal Pulmonary Venous Connections
Diagnostic Testing. Invasive
Pulmonary Venous Pathology

Year of Publication: 1975

Age Focus: Pediatric

Article Type: Case Reports or Retrospective Observations in Small Groups of Patients (≤10 patients)

Article Access: Free PDF File or Full Text Article Available Through PubMed or DOI: No