All Categories

Infantile Scimitar Syndrome With Contralateral Pulmonary Vein Stenosis and Refractory Pulmonary Hypertension

Janelle Buysse, Ramya Deepthi Billa, Daniel McLennan, Ravi Ashwath, Aditya Badheka, Madhuradhar Chegondi University of Iowa Stead Family Children’s Hospital.United States CureusCureus 2021; 13DOI: 10.7759/cureus.17203 AbstractInfantile scimitar syndrome is associated with pulmonary hypertension which can be difficult to manage. We present a three-month-old infant with scimitar syndrome, who eventually developed refractory pulmonary hypertension, posing a significant […]

Infantile Scimitar Syndrome With Contralateral Pulmonary Vein Stenosis and Refractory Pulmonary Hypertension Read More »

This and that: management of Tetralogy of Fallot and pulmonary vein stenosis in an infant-a case report

Christopher P. Scott, Kamel Shibbani, Christopher A. Caldarone, Daniel McLennan Children’s Wisconsin. University of Iowa Stead Family Children’s Hospital. Texas Children’s Hospital.United States European Heart Journal Case ReportsEur Heart J Case Rep 2021; 5DOI: 10.1093/ehjcr/ytab429 AbstractBackground: Tetralogy of Fallot (TOF) is the most common congenital cyanotic cardiac lesion. Pulmonary vein stenosis occurs much less commonly and remains

This and that: management of Tetralogy of Fallot and pulmonary vein stenosis in an infant-a case report Read More »

Effectiveness of posterior aortopexy for the left pulmonary vein obstruction between the left atrium and the descending aorta

Kwang Ho Choi, Hyungtae Kim, Si Chan Sung, Hyoung Doo Lee, Hoon Ko, Joung-Hee Byun Pusan National University Yangsan Hospital.Republic of Korea Journal of Cardiac SurgeryJ Card Surg 2021; 36: 2644-2650DOI: 10.1111/jocs.15596 AbstractBackground: Left pulmonary vein (PV) obstruction can occur due to compression between the left atrium (LA) and the descending aorta (DA). One of the effective

Effectiveness of posterior aortopexy for the left pulmonary vein obstruction between the left atrium and the descending aorta Read More »

Longer Exposure to Left-to-Right Shunts Is a Risk Factor for Pulmonary Vein Stenosis in Patients with Trisomy 21

Connie Choi, Kimberlee Gauvreau, Philip Levy, Ryan Callahan, Kathy J. Jenkins, Minghui Chen Harvard Medical School and Boston Children’s Hospital.United States ChildrenChildren 2021; 8DOI: 10.3390/children8010019 AbstractWe conducted a study to determine whether patients born with Trisomy 21 and left-to-right shunts who develop pulmonary vein stenosis (PVS) have a longer exposure to shunt physiology compared to those

Longer Exposure to Left-to-Right Shunts Is a Risk Factor for Pulmonary Vein Stenosis in Patients with Trisomy 21 Read More »

Autologous vascularised pericardial flap tunneling technique in Scimitar syndrome repair with dextrocardia: lessons from the Senning procedure

Alain J. Poncelet, Karlien Carbonez, Jean E. Rubay Cliniques Universitaires Saint-Luc, Bruxelles.Belgium Cardiology in the YoungCardiol Young 2021; 31: 859-861DOI: 10.1017/S1047951120004928 AbstractScimitar syndrome is a rare variant (5%) of partial abnormal pulmonary venous return. Surgery is required when pulmonary overcirculation is present. Following repair, Scimitar vein stenosis occurs in approximately 20%. We applied a variant of

Autologous vascularised pericardial flap tunneling technique in Scimitar syndrome repair with dextrocardia: lessons from the Senning procedure Read More »

Treatment of Congenital and Acquired Pulmonary Vein Stenosis

Patcharapong Suntharos, Lourdes R. Prieto Nicklaus Children’s Hospital.United States Current Cardiology ReportsCurr Cardiol Rep 2020; 22DOI: 10.1007/s11886-020-01395-x AbstractPurpose of review: Pulmonary vein stenosis (PVS) is a rare entity that until the last 2 decades was seen primarily in infants and children. Percutaneous and surgical interventions have limited success due to relentless restenosis, and mortality remains high. In

Treatment of Congenital and Acquired Pulmonary Vein Stenosis Read More »

Progress in Pulmonary Vein Stenosis: Lessons from Success in Treating Pulmonary Arterial Hypertension

Kathy J. Jenkins, Jeffrey R. Fineman Boston Children’s Hospital. University of California, San Francisco.United States ChildrenChildren 2022; 9DOI: 10.3390/children9060799 AbstractPulmonary vein stenosis (PVS) is a rare and poorly understood condition that can be classified as primary, acquired, status-post surgical repair of PVS, and/or associated with developmental lung disease. Immunohistochemical studies demonstrate that obstruction of the large

Progress in Pulmonary Vein Stenosis: Lessons from Success in Treating Pulmonary Arterial Hypertension Read More »

Systemic Sirolimus to Prevent In-Stent Stenosis in Pediatric Pulmonary Vein Stenosis

Ryan Callahan, Jesse J. Esch, Grace Wang, Christina M. Ireland, Kimberlee Gauvreau, Kathy J. Jenkins Boston Children’s Hospital and Harvard Medical School.United States Pediatric CardiologyPediatr Cardiol 2020; 41: 282-289DOI: 10.1007/s00246-019-02253-6 AbstractEvaluate the efficacy of systemic sirolimus (rapamycin) in preventing in-stent stenosis (ISS) in pediatric intraluminal pulmonary vein stenosis (PVS). Report the adverse events related to sirolimus

Systemic Sirolimus to Prevent In-Stent Stenosis in Pediatric Pulmonary Vein Stenosis Read More »

Diagnostic performance of CT angiography to detect pulmonary vein stenosis in children

Christian A. Barrera, David Saul, Jordan B. Rapp, Christopher L. Smith, Ammie M. White, David M. Biko, Hansel J. Otero The Children’s Hospital of Philadelphia and University of Pennsylvania.United States International Journal of Cardiovascular ImagingInt J Cardiovasc Imaging 2020; 36: 141-147DOI: 10.1007/s10554-019-01693-8 AbstractTo assess the diagnostic efficiency of CT angiography (CTA) to detect pulmonary vein stenosis

Diagnostic performance of CT angiography to detect pulmonary vein stenosis in children Read More »

Long-term outcome of percutaneous intervention for pulmonary vein stenosis after pulmonary vein isolation procedure

Patcharapong Suntharos, Sarah E. Worley, Wei Liu, Marion Siperstein, Lourdes R. Prieto Nicklaus Children’s Hospital. Cleveland Clinic Foundation.United States Catheterization and Cardiovascular InterventionsCatheter Cardiovasc Interv 2020; 95: 389-397DOI: 10.1002/ccd.28628 AbstractObjectives: Report long-term outcomes of percutaneous intervention in patients with pulmonary vein stenosis (PVS) after pulmonary vein isolation (PVI) from a single center over 16 years.Background: Outcome reports of

Long-term outcome of percutaneous intervention for pulmonary vein stenosis after pulmonary vein isolation procedure Read More »