Length of Life Associated with Pulmonary Venous Obstruction

Systemic Sirolimus Therapy for Infants and Children With Pulmonary Vein Stenosis

Jay D. Patel, Michael Briones, Mansi Mandhani, Shannon Jones, Divya Suthar, Rosemary Gray, Joelle Pettus, Courtney McCraken, Amanda Thomas, Christopher J. Petit Emory University and Children’s Healthcare of AtlantaUnited States Journal of the American College of CardiologyJ Am Coll Cardiol 2021; 77: 2807-2818DOI: 10.1016/j.jacc.2021.04.013 AbstractBackground: Anatomic interventions for pulmonary vein stenosis (PVS) in infants and children have […]

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Multifactorial pulmonary hypertension in infantile scimitar syndrome

Damien Bonnet, Isabelle Szezepanski, Christophe Delacourt, Sophie Malkezadeh-Milani, Maryline Lévy Hôpital Necker-Enfants Malades, AP-HP, Université de ParisFrance Archives of Cardiovascular DiseaseArch Cardiovasc Dis 2022; 115: 142-150DOI: 10.1016/j.acvd.2022.01.004 AbstractBackground: Pulmonary hypertension in infantile scimitar syndrome is highly prevalent at diagnosis, and has a multifactorial origin.Aims: To analyse the constellation of anatomical anomalies and initial physiology, and their contribution

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Reintervention and mortality risk after total anomalous pulmonary venous connection repair

Kevin M. Beers, Christian P. Jacobson, Stewart R. Miller, David G. Lehenbauer, Elaine Maldonado, S. Adil Husain, John H. Calhoon University of Texas Health San Antonio.United States Cardiology in the YoungCardiol Young 2023; Online ahead of printDOI: 10.1017/S1047951122004280 AbstractBackground: Management of total anomalous pulmonary venous connections has been extensively studied to further improve outcomes. Our institution previously

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Association between pulmonary vein stenosis and necrotizing enterocolitis or gastrointestinal pathology: A case-control study

Jennifer Duchon, Christiana Farkouh‑Karoleski, Dominique D. Bailey, Usha S. Krishnan Bronx Care Hospital System. Columbia University Irving Medical Center. Valley Health System.United States Annals of Pediatric CardiologyAnn Pediatr Cardiol 2022; 15: 13-19DOI: 10.4103/apc.apc_210_21 AbstractObjective: Pulmonary vein stenosis (PVS) is an emerging cause of pulmonary hypertension in preterm infants. It is an often lethal condition with poor long.term

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Acute Pulmonary Vasodilator Testing and Long-Term Clinical Course in Segmental Pulmonary Vascular Disease

Liezl Domingo, H. Sonali Magdo, Ronald W. Day University of Utah and Primary Children’s Hospital.United States Pediatric CardiologyPediatr Cardiol 2018; 39: 501-508DOI: 10.1007/s00246-017-1780-9 AbstractResults of acute pulmonary vasodilator testing (AVT) and the outcome of medical therapy have not been described in patients with segmental pulmonary vascular disease (SPVD). We sought to compare the pulmonary vasodilatory effects

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Surgical and Cardiac Catheterization Outcomes of Scimitar Syndrome Patients: A Three Decade Single-Center Experience

Emma Seymour, George Mallory, Raysa Morales-Demori Baylor College of Medicine and Texas Children’s Hospital.United States Pediatric CardiologyPediatr Cardiol 2023; 44: 579-586DOI: 10.1007/s00246-022-02965-2 AbstractScimitar syndrome (SS) is a rare congenital condition which includes partial anomalous pulmonary venous return (PAPVR) and a variable degree of pulmonary hypoplasia. We describe the clinical features, therapeutic approach and outcomes of patients

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Treatment and prognosis of Scimitar syndrome: A retrospective analysis in a single center of East China

Kai Wang, Xinyi Xu, Tingliang Liu, Wei Gao, Ying Guo Shanghai Children’s Medical Center and Shanghai Jiao Tong University. The First Affiliated Hospital of Wenzhou Medical University.China Frontiers in Cardiovascular MedicineFront Cardiovasc Med 2022;DOI: 10.3389/fcvm.2022.973796 AbstractBackground: Scimitar syndrome is a rare congenital cardiovascular malformation; its optimal management remains controversial. This study aims to present the clinical experience

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Total Anomalous Pulmonary Venous Connection Repair: Single-Center Outcomes in a Lower-Middle Income Region

Praveen Reddy Bayya, Shruti Varghese, Jessin Puliparambil Jayashankar, Abish Sudhakar, Rakhi Balachandran, Brijesh Parayaru Kottayil, Balaji Srimurugan, Praveen Kerala Varma, Praveen Kumar Neema, R. Krishna Kumar Amrita Institute of Medical Sciences and Research CentreIndia World Journal for Pediatric and Congenital Heart SurgeryWorld J Pediatr Congenit Heart Surg 2022; 13: 458-465DOI: 10.1177/21501351221103492 AbstractBackground: The management of total anomalous

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Cardiac surgical outcomes of patients with heterotaxy syndrome

Manan H. Desai, Nicolle M. Ceneri, Zaenab Dhari, Aybala Tongut, Mahmut Ozturk, Steven J. Staffa, David Zurakowski, David Schidlow, Pranava Sinha, Richard A. Jonas, Can Yerebakan Children’s National Hospital and George Washington University School of Medicine and Health Sciences. Boston Children’s Hospital and Harvard Medical School.United States Journal of Thoracic and Cardiovascular Surgery OpenJTCVS Open

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Pulmonary vein stenosis: Treatment and challenges

Rachel D. Vanderlaan, Jonathan Rome, Russel Hirsch, Dunbar Ivy, Christopher A. CaldaroneHospital for Sick Children. Children’s Hospital of Philadelphia. Cincinnati Children’s Hospital. Children’s Hospital Colorado. Texas Children’s Hospital and Baylor College of Medicine.Canada and United States Journal of Thoracic and Cardiovascular SurgeryJ Thorac Cardiovasc Surg 2021; 161: 2169-2176DOI: 10.1016/j.jtcvs.2020.05.117 AbstractNo Abstract CategoryStenosis or Obstruction of Normal

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