Age Focus: Pediatric

Congenital atresia of unilateral pulmonary veins associated with a single ventricle: a rare case report and literature review

Hsing-Yuan Lee, Betau Hwang, Pi-Chang Lee, Sheng-Ling Jan, C.C. Laura Meng Taoyuan Armed Force General Hospital.Taiwan Circulation JournalCirc J 2008; 72: 1544-1546DOI: 10.1253/circj.cj-07-0516 AbstractCongenital atresia or extreme hypoplasia of individual pulmonary veins is a rare condition that is usually asymptomatic if it only involves 1 or 2 segments of the lungs. It may be fatal if […]

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Acquired unilateral pulmonary vein atresia in a 3-year-old boy

Mohammed Firdouse, Arnav Agarwal, Lars Grosse-Wortmann, Tapas K. Mondal University of Toronto and Hospital for Sick Children. McMaster University McMaster Children’s Hospital.Canada Journal of UltrasoundJ Ultrasound 2014; 18: 73-78DOI: 10.1007/s40477-014-0135-0 AbstractWhile unilateral pulmonary venous atresia (UPVA) most commonly presents as an extremely rare late embryological defect resulting in complete occlusion or absence of the PV pathway,

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Unilateral absence of the pulmonary veins: an unusual diagnosis with characteristic imaging findings

Terry L. Levin, Bradford W. Betz, Lisa M. Gennarini, Chana Wircberg Children’s Hospital of Montefiore Medical Center. United States Clinical ImagingClin Imaging 2019; 55:107-111DOI: 10.1016/j.clinimag.2019.01.022 AbstractBackground: Congenital unilateral absence of the pulmonary vein (UCAPV) is a rare entity with characteristic clinical and imaging findings. Despite its congenital nature, the radiographic findings and symptoms of UCAPV may not

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A 12-Year-Old Girl With Dyspnea and Unilateral Interlobular Septal Thickening

Yong Chen, Yao Xiao, Ying Zhang, Guangfa Zhu, Ruiyu Dou, Hong Gu Beijing Anzhen Hospital and Capital Medical University.China ChestChest 2019; 156: e57-e61DOI: 10.1016/j.chest.2019.03.022 AbstractA 12-year-old girl was admitted to the hospital for exercise intolerance and radiographic abnormalities. She presented with a 5-year history of shortness of breath during intense exercise and did not undergo any

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Diagnosis and management of congenital right pulmonary venous atresia

I. Ricardo Argueta-Morales, Ruchira Garg, William M. DeCampli Miami Children’s Hospital and Arnold Palmer Hospital for Children.United States Cardiology in the YoungCardiol Young 2009; 19: 648-651DOI: 10.1017/S1047951109991867 AbstractCongenital unilateral pulmonary venous atresia is a rare anatomical defect. Patients present with pulmonary symptoms, and diagnosis may be elusive. Pulmonary arterial wedge angiography is the gold standard with

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Right Pulmonary Venous Atresia: A Rare Cause for Recurrent Unilateral Pneumonia

Prashant P. Patil Lotus Children Hospital.India Journal of Clinical and Diagnostic ResearchJ Clin Diag Res 2017; 11: DOI: 10.7860/JCDR/2017/25670.10596 AbstractRecurrent unilateral pneumonia poses a diagnostic dilemma for all paediatricians. Isolated pulmonary venous atresia is an uncommon entity, which presents with recurrent unilateral pulmonary infections, dyspnoea on exertion and haemoptysis. It is associated with significant mortality and

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Unilateral pulmonary vein atresia presenting with recurrent hemoptysis and bronchial varices in an Ethiopian adolescent: a case report

Abate Yeshidinber Weldetsadik, Abdi Kebede, Binyam Gebremedhin Godu, Maru Gama Saint Paul’s Hospital Millennium Medical College. Ethiopia Journal of Medical Case ReportsJ Med Case Rep 2023; 17:DOI: 10.1186/s13256-023-03956-4 AbstractBackground: Congenital unilateral pulmonary vein atresia is a rare anomaly resulting from failure of the pulmonary vein to incorporate in the left atrium. It is a very rare cause

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Unilateral pulmonary vein atresia: A rare case of hemoptysis

Cindy S. DeMastes-Crabtree, Edward Kim, Ronald L. Morton University of Louisville and Kosair Children’s Hospital. United States Respiratory Medicine Case ReportsRespir Med Case Rep 2015; 15: 83-84DOI: 10.1016/j.rmcr.2015.05.009 AbstractWe present a rare case of hemoptysis secondary to isolated unilateral pulmonary vein atresia. Isolated pulmonary vein atresia is a rare condition in which patients typically acquire a

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Congenital unilateral pulmonary vein atresia: A rare disease with successful outcome in a child

Raja Sumandatta Aduri, Javid Raja, Ganesh Kumar Munirathinam, Raghuraman Soundararajan, Arun Sharma, Sachin Mahajan 29751Postgraduate Institute of Medical Education and Research.India Asian Cardiovascular and Thoracic AnnalsAsian Cardiovasc Thorac Ann 2022; 30: 943-946DOI: 10.1177/02184923221115972 AbstractUnilateral pulmonary vein atresia is a rare congenital anomaly that may occur in association with other congenital heart diseases. We report a rare

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Isolated unilateral pulmonary vein atresia with hemoptysis in a child: A case report and literature review

Changqing Tang, Hongyu Duan, Kaiyu Zhou, Yimin Hua, Xiaoliang Liu, Yifei Li, Chuan Wang West China Institute of Women and Children’s Health, West China Second University Hospital, Sichuan University West China Medical School of Sichuan University. China MedicineMedicine 2018; DOI: 10.1097/MD.0000000000011882 AbstractRationale: Hemoptysis is an uncommon chief complaint but a distressing symptom in pediatric patients. Due to

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