Age Focus: Pediatric

Congenital unilateral pulmonary vein atresia: A rare disease with successful outcome in a child

Raja Sumandatta Aduri, Javid Raja, Ganesh Kumar Munirathinam, Raghuraman Soundararajan, Arun Sharma, Sachin Mahajan 29751Postgraduate Institute of Medical Education and Research.India Asian Cardiovascular and Thoracic AnnalsAsian Cardiovasc Thorac Ann 2022; 30: 943-946DOI: 10.1177/02184923221115972 AbstractUnilateral pulmonary vein atresia is a rare congenital anomaly that may occur in association with other congenital heart diseases. We report a rare […]

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Isolated unilateral pulmonary vein atresia with hemoptysis in a child: A case report and literature review

Changqing Tang, Hongyu Duan, Kaiyu Zhou, Yimin Hua, Xiaoliang Liu, Yifei Li, Chuan Wang West China Institute of Women and Children’s Health, West China Second University Hospital, Sichuan University West China Medical School of Sichuan University. China MedicineMedicine 2018; DOI: 10.1097/MD.0000000000011882 AbstractRationale: Hemoptysis is an uncommon chief complaint but a distressing symptom in pediatric patients. Due to

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[Thoracic imaging features of congenital unilateral pulmonary vein atresia]

Yifan Guo, Chengbin He, Jianmin Cheng, Fenglei Dong, Bo Ghen Second Affiliated Hospital and Yuying Children’s Hospital of Wenzhou Medical University.China International Journal of Medical RadiologyInt J Med Radiol 2019; 42: 94-98DOI10.19300/j.2019.L6057; AbstractObjective: To investigate the thoracic imaging features of congenital unilateral pulmonary venous atresia (UPVA). Methods: Clinical manifestations and imaging features of two patients

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Mediastinal and hilar soft tissue mass-like lesions in congenital unilateral pulmonary vein atresia: A retrospective review of seven pediatric patients

Reiko Okamoto, Osamu Miyazaki, Hidekazu Aoki, Yoshiyuki Tsutsumi, Mikiko Miyasaka, Minako Hoshiai, Shunsuke Nosaka National Center for Child Health and Development. Yamanashi Prefectural Central Hospital.Japan Pediatrics InternationalPediatr Int 2020; 62: 1234-1240DOI: 10.1111/ped.14307 AbstractBackground: Congenital unilateral pulmonary vein atresia (CUPVA) is known to lead to the formation of an abnormal confluent mediastinal and hilar soft tissue mass, thoracic

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Unilateral pulmonary vein atresia: diagnostic dilemma unfolded on imaging

Basavaraj Biradar, Arun Sharma, Amarinder Singh Malhi, Sanjeev Kumar All India Institute of Medical Sciences.India British Medical Journal Case ReportsBMJ Case Rep 2018;DOI: 10.1136/bcr-2017-224154 AbstractUnilateral pulmonary vein atresia is a rare entity, usually congenital in origin. It is thought to result from failure of incorporation of common pulmonary vein to left atrium. Patients often present with

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Unilateral pulmonary vein atresia presenting with recurrent haemoptysis in a child: a case report

Martin Ngie Liong Wong, Ing Ping Tang, Yek Kee Chor, Kiew Siong Lau, Anne Rachel John, King Ching Hii, Olive Pei Yi Lee, Wooi Kok Lim, Hannah Pei Koon Tan Sarawak Heart Center. Universiti Malaysia. Sarawak General Hospital. Miri Hospital.Malaysia BioMedical Central PediatricsBMC Prediatr 2020; 20:DOI: 10.1186/s12887-020-02348-7 AbstractBackground: Haemoptysis is an uncommon presenting symptom in children and

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Imaging findings of an asymptomatic child with pulmonary vein atresia

Taísa Davaus Gasparetto, Pedro Daltro, Edson Marchiori Federal University of Rio de Janeiro.Brazil Pediatric RadiologyPediatr Radiol 2010; 40: 1458-1459DOI: 10.1007/s00247-010-1663-1 AbstractAbstract Not Available CategoryAbsence or Atresia of Normal Pulmonary Venous ConnectionsDiagnostic Testing. NoninvasiveSymptoms and Quality of Life Associated with Pulmonary Venous Obstruction Year of Publication: 2010 Age Focus: Pediatric Article Type: Case Reports or Retrospective Observations in Small Groups

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Unilateral Pulmonary Vein Atresia in a Child

Jia-Bei Liu, Peng Liu First Affiliated Hospital of Hunan Normal University and Hunan Provincial People’s Hospital.China Pediatric PulmonologyPediatr Pulmonol 2025; 60: DOI: 10.1002/ppul.27378 AbstractWe describe a case of unilateral pulmonary vein atresia in a child who presented with a recurrent cough. Pulmonary artery CT angiography confirmed the diagnosis. In addition, we found anomalous blood-supplying arteries from

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Unilateral pulmonary vein atresia

Y. Wang, Y. Tang, L. Sun, X. Zhang, Y. Liu, S. Xu, Y. Su, L. Zhang, X. Tang, H. Yang, Yuelin Shen Henan Children’s Hospital, Zhengzhou Children’s Hospital and Zhengzhou University. Capital Medical University and National Center for Children’s Health. Children’s Hospital of Xinjang Uygur Autonomous Region, Xinjiang Hospital of Beijing Children’s Hospital and Seventh

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Prognostic factors in pediatrics TAPVC: a 10-year retrospective study

Xiaoying Xue, Wen Ling, Qiumei Wu, Biying Huang, Shan Guo, Zongjie Weng Fujian Maternity and Child Health Hospital and Fujian Medical University.China Scientific ReportsSci Rep 2025; 15: DOI: 10.1038/s41598-025-94619-5 AbstractTotal anomalous pulmonary venous connection (TAPVC) is a rare congenital heart defect where the pulmonary veins abnormally connect to the systemic venous circulation, rather than the left

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