Age Focus: Pediatric

Effectiveness of posterior aortopexy for the left pulmonary vein obstruction between the left atrium and the descending aorta

Kwang Ho Choi, Hyungtae Kim, Si Chan Sung, Hyoung Doo Lee, Hoon Ko, Joung-Hee Byun Pusan National University Yangsan Hospital.Republic of Korea Journal of Cardiac SurgeryJ Card Surg 2021; 36: 2644-2650DOI: 10.1111/jocs.15596 AbstractBackground: Left pulmonary vein (PV) obstruction can occur due to compression between the left atrium (LA) and the descending aorta (DA). One of the effective […]

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Longer Exposure to Left-to-Right Shunts Is a Risk Factor for Pulmonary Vein Stenosis in Patients with Trisomy 21

Connie Choi, Kimberlee Gauvreau, Philip Levy, Ryan Callahan, Kathy J. Jenkins, Minghui Chen Harvard Medical School and Boston Children’s Hospital.United States ChildrenChildren 2021; 8DOI: 10.3390/children8010019 AbstractWe conducted a study to determine whether patients born with Trisomy 21 and left-to-right shunts who develop pulmonary vein stenosis (PVS) have a longer exposure to shunt physiology compared to those

Longer Exposure to Left-to-Right Shunts Is a Risk Factor for Pulmonary Vein Stenosis in Patients with Trisomy 21 Read More »

Autologous vascularised pericardial flap tunneling technique in Scimitar syndrome repair with dextrocardia: lessons from the Senning procedure

Alain J. Poncelet, Karlien Carbonez, Jean E. Rubay Cliniques Universitaires Saint-Luc, Bruxelles.Belgium Cardiology in the YoungCardiol Young 2021; 31: 859-861DOI: 10.1017/S1047951120004928 AbstractScimitar syndrome is a rare variant (5%) of partial abnormal pulmonary venous return. Surgery is required when pulmonary overcirculation is present. Following repair, Scimitar vein stenosis occurs in approximately 20%. We applied a variant of

Autologous vascularised pericardial flap tunneling technique in Scimitar syndrome repair with dextrocardia: lessons from the Senning procedure Read More »

Progress in Pulmonary Vein Stenosis: Lessons from Success in Treating Pulmonary Arterial Hypertension

Kathy J. Jenkins, Jeffrey R. Fineman Boston Children’s Hospital. University of California, San Francisco.United States ChildrenChildren 2022; 9DOI: 10.3390/children9060799 AbstractPulmonary vein stenosis (PVS) is a rare and poorly understood condition that can be classified as primary, acquired, status-post surgical repair of PVS, and/or associated with developmental lung disease. Immunohistochemical studies demonstrate that obstruction of the large

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Systemic Sirolimus to Prevent In-Stent Stenosis in Pediatric Pulmonary Vein Stenosis

Ryan Callahan, Jesse J. Esch, Grace Wang, Christina M. Ireland, Kimberlee Gauvreau, Kathy J. Jenkins Boston Children’s Hospital and Harvard Medical School.United States Pediatric CardiologyPediatr Cardiol 2020; 41: 282-289DOI: 10.1007/s00246-019-02253-6 AbstractEvaluate the efficacy of systemic sirolimus (rapamycin) in preventing in-stent stenosis (ISS) in pediatric intraluminal pulmonary vein stenosis (PVS). Report the adverse events related to sirolimus

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Diagnostic performance of CT angiography to detect pulmonary vein stenosis in children

Christian A. Barrera, David Saul, Jordan B. Rapp, Christopher L. Smith, Ammie M. White, David M. Biko, Hansel J. Otero The Children’s Hospital of Philadelphia and University of Pennsylvania.United States International Journal of Cardiovascular ImagingInt J Cardiovasc Imaging 2020; 36: 141-147DOI: 10.1007/s10554-019-01693-8 AbstractTo assess the diagnostic efficiency of CT angiography (CTA) to detect pulmonary vein stenosis

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Scimitar syndrome: A new multipatch technique and incidence of postoperative pulmonary vein obstruction

Robert L. Geggel, Kimberlee Gauvreau, Ryan Callahan, Eric N. Feins, Christopher W. Baird Boston Children’s Hospital and Harvard Medical School.United States Journal of Thoracic and Cardiovascular Surgery TechniquesJTCVS Tech 2020; 4: 208-216DOI: 10.1016/j.xjtc.2020.07.027 AbstractObjective: A review of our center’s experience before March 2011 showed that one half of 36 patients who had a baffling or reimplantation procedure

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Transcatheter Recanalization of Atretic Pulmonary Veins in Infants and Children

Jay D. Patel, Mansi Mandhani, Rosemary Gray, Joelle Pettus, Courtney E. McCracken, Amanda Thomas, Holly Bauser-Heaton, Dennis W. Kim, Christopher J. Petit Emory University and Children’s Healthcare of Atlanta. Columbia University Vagelos College of Physicians and Surgeons and NewYork-Presbyterian Morgan Stanley Children’s Hospital.United States Circulation Cardiovascular InterventionsCirc Cardiovasc Interv 2022; 15DOI: 10.1161/CIRCINTERVENTIONS.121.011351 AbstractBackground: Pulmonary vein stenosis is a progressive disease associated with a high rate of mortality in children. If left

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Left hypoplastic lung and hemoptysis-rare familial unilateral pulmonary vein atresia

Ronly Har-Even Cohn, Matthew Hicks, Atilano Lacson, Anne Hicks University of Alberta.Canada Clinical Case ReportsClin Case Rep 2020; 8: 1698-1703DOI: 10.1002/ccr3.2982 AbstractUnilateral pulmonary vein atresia (UPVA) is a rare congenital vascular malformation with obliteration of the pulmonary vein. We present a case series of three siblings with variable presentation of UPVA. We suggest a dominant genetic cause based on different

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Changes in Prognosis of Heterotaxy Syndrome Over Time

Puja Banka, Adi Adar, Barbara Schaetzle, Lynn A. Sleeper, Sitaram Emani, Tal Geva Boston Children’s Hospital and Harvard University.United States PediatricsPediatrics 2020; 146DOI: 10.1542/peds.2019-3345 AbstractBackground: Long-term outcomes in heterotaxy syndrome (HS) are poorly described. Some reports suggest improved survival in the recent era, whereas others do not. We sought to describe long-term outcomes and assess whether outcomes

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