Pulmonary Hypertension Associated with Stenosis or Atresia of Pulmonary Veins

Case Report: Post-Total anomalous pulmonary venous connection pulmonary hypertension – novel treatment using sirolimus and atrial flow regulator implantation

Stasa Krasic, Antony Hermuzi, Ivan Dizdarevic, Vesna Topic, Nevena Djorovic, Mihail Basa, Vladislav Vukomanovic Mother and Child Health Institute of Serbia and University of Belgrade. Freeman Hospital and Newcastle upon Tyne Hospitals NHS Foundation Trust.Serbia and United Kingdom Frontiers in Cardiovascular MedicineFront Cardiovasc Med 2026; 13:DOI: 10.3389/fcvm.2026.1783773 AbstractObjective: In patients who have undergone surgical repair of TAPVC […]

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Losartan attenuates upstream vasculopathy in a modified piglet model of pulmonary vein stenosis: contribution of the Hippo pathway

Wenhui Zeng, Siming Liu, Zhen Xu, Fangbao Ding, Ju Mei, Jiaquan Zhu Xinhua Hospital, Shanghai Jiaotong University School of Medicine.China Annals of Translational MedicineAnn Transl Med 2022; DOI: 10.21037/atm-22-2621 AbstractBackground: Diffuse pulmonary vein stenosis (PVS) is an intractable congenital heart disease for which the underlying mechanism remains unclear. In this study, we investigated the effect of losartan

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Swine model of chronic postcapillary pulmonary hypertension with right ventricular remodeling: long-term characterization by cardiac catheterization, magnetic resonance, and pathology

Daniel Pereda, Ana Garcia-Alvarez, Damián Sánchez-Quintana, Mario Nuño, Leticia Fernández-Friera, Rodrigo Fernández-Jiménez, José Manuel García Ruíz, Elena Sandoval, Jaume Aguero, Manuel Castellá. Roger J. Hajjar, Valentín Fuster, Borja Ibáñez Centro Nacional de Investigaciones Cardiovasculares Carlos III.Spain Journal of Cardiovascular Translational ResearchJ Cardiovasc Transl Res 2014; 7: 494-506DOI: 10.1007/s12265-014-9564-6 AbstractPulmonary hypertension (PH) is prevalent and carries high

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Pericardial effusion and pulmonary vein stenosis in severe bronchopulmonary dysplasia

Emma E. Williams, Mahesh Nanjundappa, Kunal Babla, James Wong, Theodore Dassios, Anne Greenough King’s College London and King’s College Hospital NHS Foundation Trust. Evelina Children’s Hospital and Guy’s and St Thomas’ NHS Foundation Trust.United Kingdom Archives of Disease in Children Fetal and Neonatal EditionArch Dis Child Fetal Neonatal Ed 2022; 107: DOI: 10.1136/archdischild-2021-321830 AbstractAbstract Not Available

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Pulmonary vein stenosis in a child with ventricular septal defect

Sarvesh Pal Singh, Poonam Malhotra Kapoor, Velayoudham Devagourou All India Institute of Medical Sciences. India Asian Cardiovascular and Thoracic AnnalsAsian Cardiovasc Thorac Ann 2014; 22: 1130-1131DOI: 10.1177/0218492313513600 AbstractAbstract Not Available CategoryStenosis or Obstruction of Normal Pulmonary Venous ConnectionsPulmonary Hypertension Associated with Stenosis or Atresia of Pulmonary VeinsPatient Factors Influencing the Onset, Severity or Outcome of DiseaseDiagnostic

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Outcome predictors and implications for management of scimitar syndrome

Susan M. Dusenbery, Tal Geva, Anna Seale, Anne Marie Valente, Jing Zhou, Laureen Sena, Robert L. Geggel Boston Children’s Hospital.United States American Heart JournalAm Heart J 2013; 165: 770-777DOI: 10.1016/j.ahj.2013.01.016 AbstractBackground: Scimitar syndrome is a rare congenital anomaly. We evaluated risk factors for postoperative pulmonary vein stenosis or death and predictive factors for survival without scimitar vein

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Primary pulmonary vein stenosis in a premature infant without bronchopulmonary dysplasia: a case report

Lijian Xie, Tingting Xiao, Jie Shen Shanghai Children’s Hospital and Shanghai Jiao Tong University. China Heart and LungHeart Lung 2014; 43: 367-370DOI: 10.1016/j.hrtlng.2014.04.018 AbstractPrimary pulmonary vein stenosis (PVS) presenting in childhood is uncommon and is related to premature with bronchopulmonary dysplasia (BPD). Here we present a premature infant with primary PVS and without BPD. In our

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Scimitar syndrome presenting in infancy

Charles B. Huddleston, Vernat Exil, Charles E. Canter, Eric N. Mendeloff Washington University School of Medicine and St. Louis Children’s Hospital.United States Annals of Thoracic SurgeryAnn Thorac Surg 1999; 67: 154-159DOI: 10.1016/s0003-4975(98)01227-2 AbstractBackground: Scimitar syndrome has a variable presentation based on the age at which the diagnosis is made. In general, infants presenting in heart failure have

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A Novel Rat Model for Group 2 Pulmonary Hypertension by Total Pulmonary Vein Banding: Multi-Omics Insights into Pathophysiological Mechanisms

Jin Shentu, Wenxuan Dai, Chang Chen, Jiawei Huang, Lijun Chen, Yi Yan, Han Zhang, Zhongqun Zhu, Guocheng Shi, Huiwen Chen Shanghai Children’s Medical Center and Shanghai Jiao Tong University School of Medicine.China Journal of Thoracic and Cardiovascular SurgeryJ Thorac Cardiovasc Surg 2026;DOI: 10.1016/j.jtcvs.2026.01.017 AbstractObjectives: Group 2 pulmonary hypertension (PH) remains a highly morbid disease, yet no specific

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Scimitar syndrome in infancy

Yon-An Gao, Patricia E. Burrows, Lee N. Benson, Marlene Rabinovitch, Robert M. Freedom Hospital for Sick Children.Canada Journal of the American College of CardiologyJ Am Coll Cardiol 1993; 22: DOI: 10.1016/0735-1097(93)90206-g AbstractObjectives: The objectives of this study were to determine the anatomic and physiological factors most responsible for the severe symptoms and poor prognosis of infants with

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