Pulmonary Hypertension Associated with Stenosis or Atresia of Pulmonary Veins

Pulmonary vein stenosis with Down syndrome: a rare and frequently fatal cause of pulmonary hypertension in infants and children

Srinath Gowda, Deepti Bhat, Zhuang Feng, Chung-Ho Chang, Robert D. Ross The Children’s Hospital of Michigan and Detroit Medical Center.United States Congenital Heart DiseaseCongenit Heart Dis 2014; 9: E90-E97DOI: 10.1111/chd.12088 AbstractDown syndrome (DS) patients are prone to pulmonary hypertension (PHTN) due to various cardiopulmonary causes. However, the association of DS with pulmonary vein stenosis (PVS) is […]

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An infant with primary pulmonary vein stenosis, associated with fatal occlusion of intraparenchymal small pulmonary veins

Takanari Fujii, Hideshi Tomita, Hiroaki Kise, Kazuto Fujimoto, Kozue Kobayashi, Yoshitaka Watanabe, Takeshi Yamazaki, Takeshi Shimizu, Shunsuke Sakurai, Satoshi Hibino, Junya Iwasaki, Takashi Soga, Shigeru Uemura, Kazuo Itabashi, Shigeo Yamaki Showa University Northern Yokohama Hospital. Japanese Research Institute of Pulmonary Vasculature.Japan Journal of Cardiology CasesJ Cardiol Cases 2013; 9: 3-7DOI: 10.1016/j.jccase.2013.08.013 AbstractPrimary pulmonary vein stenosis (PVS)

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Pulmonary hypertension in bronchopulmonary dysplasia: clinical findings, cardiovascular anomalies and outcomes

Maria Jesus del Cerro, Anna Sabate Rotes, Antonio Carton, Lucia Deiros, Montserrat Bret, Malaika Cordeiro, Cristina Verdu, Maria Isabel Barrios, Luis Albajara, Federico Gutierrez-Larraya La Paz Children’s Hospital.Spain Pediatric PulmonologyPediatr Pulmonol 2014; 49: 49-59DOI: 10.1002/ppul.22797 AbstractObjective: Pulmonary hypertension (PH) worsens the prognosis of bronchopulmonary dysplasia (BPD). The following items have not been fully established for PH in

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Abnormalities in embryological development in total anomalous pulmonary venous connection. A case report

Mihaela Balgradean, Eliza Cinteza, C. Cirstoveanu, Augustina Enculescu, Doina Plesca “Marie Skĺodowska-Curie” Emergency Children’s Hospital.Romania Romanian Journal of Morphology and EmbryologyRom J Morphol Embryol 2013; 54: 635-637DOI: Not Available AbstractPulmonary venous system development starts early in embryonic life. Abnormalities in the development of pulmonary venous system occur either by the absence of common pulmonary vein

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Role of left atrial hypertension in pulmonary hypertension associated with bronchopulmonary dysplasia

Rachel T. Sullivan, Megha D. Tandel, Shazia Bhombal, Gregory T. Adamson, Derek B. Boothroyd, Michael Tracy, Amanda Moy, Rachel K. Hopper Vanderbilt University Medical Center. Stanford University.United States Frontiers in PediatricsFront Pediatr 2022;DOI: 10.3389/fped.2022.1012136 AbstractLeft atrial hypertension (LAH) may contribute to pulmonary hypertension (PH) in premature infants with bronchopulmonary dysplasia (BPD). Primary causes of LAH in

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Total anomalous pulmonary venous connection: morphology and outcome from an international population-based study

Anna N. Seale, Hideki Uemura, Steven A. Webber, John Partridge, Michael Roughton, Siew Y. Ho, Karen P. McCarthy, Sheila Jones, Lynda Shaughnessy, Jan Sunnegardh, Katarina Hanseus, Hakan Berggren, Sune Johansson, Michael L. Rigby, Barry R. Keeton, Piers E. F. Daubeney, on behalf of the British Congenital Cardiac Association Royal Brompton Hospital.United Kingdom and Sweden CirculationCirculation 2010; 122: 2718-2726DOI: 10.1161/CIRCULATIONAHA.110.940825 AbstractBackground: Late mortality after repair of total anomalous pulmonary venous connection is frequently associated with pulmonary venous

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A mother and daughter with the p.R443X mutation of mucopolysaccharidosis type II: Genotype and phenotype analysis

Young Bae Sohn, Su Jin Kim, Sung Won Park, Hyung-Doo Park, Chang-Seok Ki, Chi Hwa Kim, Seung Won Huh, Sunghee Yeau, Kyung-Hoon Paik, Dong-Kyu Jin Samsung Medical Center.Republic of Korea American Journal of Medical GeneticsAm J Med Genet 2010; 152A: 3129-3132DOI: 10.1002/ajmg.a.33589 AbstractMucopolysaccharidosis type II (Hunter syndrome) is a lysosomal storage disease caused by a deficiency

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Management of pulmonary venous obstruction after correction of TAPVC: risk factors for adverse outcome

Marco Ricci, M. Elliotta, G. A. Cohen, G. Catalana, J. Stark, Mark R. de Leval, V. T. Tsang Great Ormond Street Hospital for Children NHS Trust.United Kingdom European Journal of Cardiothoracic SurgeryEur J Cardiothorac Surg 2003; 24: 28-36DOI: 10.1016/s1010-7940(03)00180-5 AbstractObjective: Recurrent pulmonary venous obstruction (PVO) occurs in 0-18% of infants undergoing correction of total anomalous pulmonary venous

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Primary pulmonary vein stenosis

D. Byron Holt, James H. Moller, Sarah Larson, Marck C. Johnson Washington University.United States American Journal of CardiologyAm J Cardiol 2007; 99: 568-572DOI: 10.1016/j.amjcard.2006.09.100 AbstractPrimary pulmonary vein stenosis (PVS) is a rare entity with a high mortality rate. Relatively little is known regarding predictors of outcome or the appropriate timing of intervention. The Pediatric Cardiac Care

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Stent implantation and subsequent dilatation for pulmonary vein stenosis in pediatric patients: maximizing effectiveness

Hideshi Tomita, Ken Watanabe, Satoshi Yazaki, Kohji Kimura, Yasuo Ono, Toshikatsu Yagihara, Shigeyuki Echigo National Cardiovascular Center.Japan Circulation JournalCirc J 2003; 67: 187-190DOI: 10.1253/circj.67.187 AbstractThe outcome of stent implantation and redilatation was investigated in 4 pediatric patients with 7 stenotic lesions of the pulmonary vein (PV), paying particular attention to late neointimal proliferation. The minimal diameter of

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