Pulmonary Hypertension Associated with Stenosis or Atresia of Pulmonary Veins

The impact of right ventricular pressure and function on survival in patients with pulmonary vein stenosis

Michelle C. Sykes, Christina Ireland, Julia E. McSweeney, Emily Rosenholm, Kristofer G. Andren, Thomas J. Kulik Boston Children’s Hospital.United States Pulmonary CirculationPulm Circ 2018;DOI: 10.1177/2045894018776894 AbstractPulmonary vein stenosis (PVS) is associated with pulmonary hypertension (PH), but there is little information regarding the impact of PH on right ventricular (RV) systolic function and survival. We conducted a […]

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Pulmonary Vein Stenosis in Neonates with Severe Bronchopulmonary Dysplasia

Natasha L. Swier, Bernadette Richards, Clifford L. Cua, Susan K. Lynch, Han Yin, Leif D. Nelin, Charles V. Smith, Carl H. Backes Ohio State University Wexner Medical Center and Nationwide Children’s Hospital. University of Washington School of Medicine.United States American Journal of PerinatologyAm J Perinatol 2016; 33: 671-677DOI: 10.1055/s-0035-1571201 AbstractObjectives: Pulmonary vein stenosis (PVS) is a rare, often lethal anomaly associated with poor

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Congenital pulmonary venous stenosis presenting as persistent pulmonary hypertension of the newborn

Robert G. Holcomb, R. Weslie Tyson, D. Dunbar Ivy, Steven H. Abman, John P. Kinsella Children’s Hospital, Denver.United States Pediatric PulmonologyPediatr Pulmonol 1999; 28: 301-306DOI: 10.1002/(sici)1099-0496(199910)28:4<301::aid-ppul10>3.0.co;2-m AbstractCongenital pulmonary venous stenosis (CPVS) has been previously described in older infants and children, typically manifesting as failure to thrive with congestive heart failure and subsequent respiratory deterioration. We report

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Intraluminal Pulmonary Vein Stenosis in Children: A “New” Lesion

Viviane G. Nasr, Ryan Callahan, Zachary Wichner, Kirsten C. Odegard, James A. DiNardo Boston Children’s Hospital.United States Anesthesia and AnalgesiaAnesth Analges 2019; 129: 27-40DOI: 10.1213/ANE.0000000000003924 AbstractPulmonary vein stenosis (PVS) is a rare disorder that leads to progressive narrowing of the extrapulmonary veins. PVS has been reported in both children and adults and in its worse iteration

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Pulmonary vein stenosis: Case report and literature review

Reshma Amin, S. Kwon, Y. Moayedi, Neil Sweezey Hospital for Sick Children.Canada Canadian Respiratory JournalCan Respir J 2009; 16: e77-e80DOI: 10.1155/2009/791653 AbstractBackground: Pulmonary vein stenosis is a rare cause of pulmonary hypertension, with variable onset and presentation. One or more of the four pulmonary veins can be primarily or secondarily affected. A five-month-old girl presented with respiratory

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Prematurity and Pulmonary Vein Stenosis: The Role of Parenchymal Lung Disease and Pulmonary Vascular Disease

Shilpa Vyas-Read, Nidhy P. Varghese, Divya Suthar, Carl Backes, Satyan Lakshminrusimha, Christopher J. Petit, Philip T. Levy Emory University and Children’s Healthcare of Atlanta. Baylor College of Medicine and Texas Children’s Hospital. Ohio State University and Nationwide Children’s Hospital. University of California Davis. Harvard University and Boston Children’s Hospital.United States Children (Basel)Children 2022; 9: 713DOI: 10.3390/children9050713

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Multifactorial pulmonary hypertension in infantile scimitar syndrome

Damien Bonnet, Isabelle Szezepanski, Christophe Delacourt, Sophie Malkezadeh-Milani, Maryline Lévy Hôpital Necker-Enfants Malades, AP-HP, Université de ParisFrance Archives of Cardiovascular DiseaseArch Cardiovasc Dis 2022; 115: 142-150DOI: 10.1016/j.acvd.2022.01.004 AbstractBackground: Pulmonary hypertension in infantile scimitar syndrome is highly prevalent at diagnosis, and has a multifactorial origin.Aims: To analyse the constellation of anatomical anomalies and initial physiology, and their contribution

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Management of Complex Pulmonary Vein Stenosis at Altitude Combining Comprehensive Percutaneous Interventional Treatment with Sirolimus, Pulmonary Hypertension Medications and Intraluminal Imaging with Optical Coherence Tomography

Michael J. Shorofsky, Gareth J. Morgan, Ernesto Mejia, Salvador A. Rodriguez, Megan Greene, Paige Sheaks, Dunbar Ivy, Jenny E. Zablah University of Colorado and Children’s Hospital Colorado.United States Pediatric CardiologyPediatr Cardiol 2023; Online ahead of printDOI: 10.1007/s00246-023-03102-3 AbstractBackground: Pulmonary vein stenosis (PVS) is a growing problem for the pediatric congenital heart population. Sirolimus has previously been shown

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Pulmonary Vein Atresia: Feasibility of Initial Recanalization Attempts with Subsequent Follow-up

Varun Aggarwal, Gary E. Stapleton, Lindsay F. Eilers, Srinath Gowda, Manish Bansal, Athar M. Qureshi, Melissa K. Webb, Asra Khan, Henri Justino Baylor College of Medicine and Texas Children’s HospitalUnited States Current Problems in CardiologyCurr Probl Cardiol 2023; 48DOI: 10.1016/j.cpcardiol.2022.101463 AbstractPulmonary vein atresia (PVA) may lead to pulmonary hypertension, cardiac failure, and death. Transcatheter or surgical treatments have rarely been offered to this population because of perceived poor outcomes. We describe single center

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Association between pulmonary vein stenosis and necrotizing enterocolitis or gastrointestinal pathology: A case-control study

Jennifer Duchon, Christiana Farkouh‑Karoleski, Dominique D. Bailey, Usha S. Krishnan Bronx Care Hospital System. Columbia University Irving Medical Center. Valley Health System.United States Annals of Pediatric CardiologyAnn Pediatr Cardiol 2022; 15: 13-19DOI: 10.4103/apc.apc_210_21 AbstractObjective: Pulmonary vein stenosis (PVS) is an emerging cause of pulmonary hypertension in preterm infants. It is an often lethal condition with poor long.term

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